Matches in SemOpenAlex for { <https://semopenalex.org/work/W1821983810> ?p ?o ?g. }
- W1821983810 endingPage "249" @default.
- W1821983810 startingPage "228" @default.
- W1821983810 abstract "Von Hippel-Lindau syndrome (VHLS) is an autosomal dominant familial cancer syndrome arising from germ-line inactivation of the VHL gene on the short arm of chromosome 3. VHLS manifests in a myriad of hyper-vascular tumors of both benign and malignant nature. Incidence of VHLS is roughly 1 in 36,000 live births and has over 90% penetrance by the age of 65. Improved understanding of the natural history and biology of VHLS has led to the introduction of screening protocols, early interventions and improved treatments, all of which resulted in a substantially improved prognosis for this disease. Further details regardingvariegated molecular pathways and mechanisms ofVHLS are emerging with the subsequent advent of novel treatment protocols that are currently in clinical trials." @default.
- W1821983810 created "2016-06-24" @default.
- W1821983810 creator A5002024579 @default.
- W1821983810 creator A5015194203 @default.
- W1821983810 creator A5025529463 @default.
- W1821983810 date "2010-01-01" @default.
- W1821983810 modified "2023-09-24" @default.
- W1821983810 title "Von Hippel Lindau Syndrome" @default.
- W1821983810 cites W129642105 @default.
- W1821983810 cites W1532143905 @default.
- W1821983810 cites W1543367609 @default.
- W1821983810 cites W1749022239 @default.
- W1821983810 cites W1844723954 @default.
- W1821983810 cites W1948708264 @default.
- W1821983810 cites W1963533810 @default.
- W1821983810 cites W1963715553 @default.
- W1821983810 cites W1965009601 @default.
- W1821983810 cites W1965690355 @default.
- W1821983810 cites W1971602109 @default.
- W1821983810 cites W1971966311 @default.
- W1821983810 cites W1972009030 @default.
- W1821983810 cites W1972032694 @default.
- W1821983810 cites W1973532066 @default.
- W1821983810 cites W1978173977 @default.
- W1821983810 cites W1980475208 @default.
- W1821983810 cites W1981184799 @default.
- W1821983810 cites W1981404227 @default.
- W1821983810 cites W1984899507 @default.
- W1821983810 cites W1985097805 @default.
- W1821983810 cites W1985949433 @default.
- W1821983810 cites W1986464453 @default.
- W1821983810 cites W1988380443 @default.
- W1821983810 cites W1989215255 @default.
- W1821983810 cites W1989228917 @default.
- W1821983810 cites W1990607537 @default.
- W1821983810 cites W1992954334 @default.
- W1821983810 cites W1994030513 @default.
- W1821983810 cites W1994326302 @default.
- W1821983810 cites W1995838314 @default.
- W1821983810 cites W1998837332 @default.
- W1821983810 cites W1999996855 @default.
- W1821983810 cites W2001943695 @default.
- W1821983810 cites W2004126278 @default.
- W1821983810 cites W2005561974 @default.
- W1821983810 cites W2006592230 @default.
- W1821983810 cites W2008946188 @default.
- W1821983810 cites W2010160635 @default.
- W1821983810 cites W2011562442 @default.
- W1821983810 cites W2012919091 @default.
- W1821983810 cites W2013394636 @default.
- W1821983810 cites W2015040639 @default.
- W1821983810 cites W2015817451 @default.
- W1821983810 cites W2018920478 @default.
- W1821983810 cites W2023891731 @default.
- W1821983810 cites W2024064023 @default.
- W1821983810 cites W2024355133 @default.
- W1821983810 cites W2026533505 @default.
- W1821983810 cites W2027705428 @default.
- W1821983810 cites W2028400858 @default.
- W1821983810 cites W2028803434 @default.
- W1821983810 cites W2029726663 @default.
- W1821983810 cites W2031485253 @default.
- W1821983810 cites W2033363278 @default.
- W1821983810 cites W2033958147 @default.
- W1821983810 cites W2035605560 @default.
- W1821983810 cites W2035734782 @default.
- W1821983810 cites W2036253788 @default.
- W1821983810 cites W2036667836 @default.
- W1821983810 cites W2039412091 @default.
- W1821983810 cites W2040031153 @default.
- W1821983810 cites W2042702043 @default.
- W1821983810 cites W2047688922 @default.
- W1821983810 cites W2050397881 @default.
- W1821983810 cites W2054141638 @default.
- W1821983810 cites W2054639131 @default.
- W1821983810 cites W2055418357 @default.
- W1821983810 cites W2056530510 @default.
- W1821983810 cites W2059742966 @default.
- W1821983810 cites W2059971436 @default.
- W1821983810 cites W2060525294 @default.
- W1821983810 cites W2061139881 @default.
- W1821983810 cites W2062608685 @default.
- W1821983810 cites W2062843221 @default.
- W1821983810 cites W2063041535 @default.
- W1821983810 cites W2063461894 @default.
- W1821983810 cites W2063897886 @default.
- W1821983810 cites W2064296340 @default.
- W1821983810 cites W2066804453 @default.
- W1821983810 cites W2067324420 @default.
- W1821983810 cites W2068555261 @default.
- W1821983810 cites W2070759851 @default.
- W1821983810 cites W2072839085 @default.
- W1821983810 cites W2073939107 @default.
- W1821983810 cites W2074820129 @default.
- W1821983810 cites W2075124527 @default.
- W1821983810 cites W2076145832 @default.
- W1821983810 cites W2080392370 @default.
- W1821983810 cites W2081460564 @default.