Matches in SemOpenAlex for { <https://semopenalex.org/work/W1487208097> ?p ?o ?g. }
- W1487208097 endingPage "151" @default.
- W1487208097 startingPage "120" @default.
- W1487208097 abstract "Bilirubin, a degradation product of heme, circulates bound to albumin, from which it is extracted in the liver. It is translocated from blood to bile by a multistep process involving hepatocellular uptake, intracellular binding, conjugation with glucuronic acid, and active transport into bile. Hyperbilirubinemias are predominantly unconjugated, mainly conjugated, or mixed. Those with normal common liver function tests are often familial and benign; abnormalities of other hepatic tests suggest a condition with potentially serious sequelae. Studies of familial hyperbilirubinemias have identified specific proteins and pathways essential for normal liver function, including bilirubin transport and metabolism. Mutations in particular proteins underlie four of the five familial hyperbilirubinemias: the Gilbert, Crigler–Najjar types 1 and 2, and Dubin–Johnson syndromes. The basis for Rotor syndrome remains unknown. Many different mutations in three protein components of the canalicular bile secretory apparatus are likewise the basis for several familial cholestasis syndromes." @default.
- W1487208097 created "2016-06-24" @default.
- W1487208097 creator A5051540329 @default.
- W1487208097 creator A5091083651 @default.
- W1487208097 date "2011-10-31" @default.
- W1487208097 modified "2023-09-27" @default.
- W1487208097 title "Bilirubin Metabolism and Jaundice" @default.
- W1487208097 cites W113763107 @default.
- W1487208097 cites W123325334 @default.
- W1487208097 cites W1483148476 @default.
- W1487208097 cites W1506454783 @default.
- W1487208097 cites W1533677192 @default.
- W1487208097 cites W1572585086 @default.
- W1487208097 cites W1592431232 @default.
- W1487208097 cites W1603478557 @default.
- W1487208097 cites W1751757376 @default.
- W1487208097 cites W175786586 @default.
- W1487208097 cites W182744212 @default.
- W1487208097 cites W1864717370 @default.
- W1487208097 cites W1880937475 @default.
- W1487208097 cites W1912745999 @default.
- W1487208097 cites W1928009957 @default.
- W1487208097 cites W193327837 @default.
- W1487208097 cites W1963856653 @default.
- W1487208097 cites W1963989090 @default.
- W1487208097 cites W1966238302 @default.
- W1487208097 cites W1966831402 @default.
- W1487208097 cites W1968911405 @default.
- W1487208097 cites W1971077247 @default.
- W1487208097 cites W1972061504 @default.
- W1487208097 cites W1973077989 @default.
- W1487208097 cites W1973385812 @default.
- W1487208097 cites W1973466019 @default.
- W1487208097 cites W1973679514 @default.
- W1487208097 cites W1973950263 @default.
- W1487208097 cites W1974055353 @default.
- W1487208097 cites W1975405461 @default.
- W1487208097 cites W1975541219 @default.
- W1487208097 cites W1977571990 @default.
- W1487208097 cites W1977842477 @default.
- W1487208097 cites W1977924630 @default.
- W1487208097 cites W1978317967 @default.
- W1487208097 cites W1979686921 @default.
- W1487208097 cites W1982410935 @default.
- W1487208097 cites W1983329266 @default.
- W1487208097 cites W1983548371 @default.
- W1487208097 cites W1984514894 @default.
- W1487208097 cites W1985264350 @default.
- W1487208097 cites W1985480034 @default.
- W1487208097 cites W1985584806 @default.
- W1487208097 cites W1987777210 @default.
- W1487208097 cites W1987859281 @default.
- W1487208097 cites W1988941552 @default.
- W1487208097 cites W1988985926 @default.
- W1487208097 cites W1989153610 @default.
- W1487208097 cites W1989847695 @default.
- W1487208097 cites W1991999803 @default.
- W1487208097 cites W1992475433 @default.
- W1487208097 cites W1998284192 @default.
- W1487208097 cites W1999785503 @default.
- W1487208097 cites W2002952355 @default.
- W1487208097 cites W2004372259 @default.
- W1487208097 cites W2004567585 @default.
- W1487208097 cites W2005085872 @default.
- W1487208097 cites W2005988754 @default.
- W1487208097 cites W2006478647 @default.
- W1487208097 cites W2007076335 @default.
- W1487208097 cites W2008117162 @default.
- W1487208097 cites W2009084021 @default.
- W1487208097 cites W2010693066 @default.
- W1487208097 cites W2011588408 @default.
- W1487208097 cites W2012021913 @default.
- W1487208097 cites W2013999141 @default.
- W1487208097 cites W2014031811 @default.
- W1487208097 cites W2015566312 @default.
- W1487208097 cites W2015968894 @default.
- W1487208097 cites W2016703262 @default.
- W1487208097 cites W2018524109 @default.
- W1487208097 cites W2019120975 @default.
- W1487208097 cites W2019532583 @default.
- W1487208097 cites W2020166192 @default.
- W1487208097 cites W2020318985 @default.
- W1487208097 cites W2022424839 @default.
- W1487208097 cites W2027001200 @default.
- W1487208097 cites W2027381646 @default.
- W1487208097 cites W2028963438 @default.
- W1487208097 cites W2030036139 @default.
- W1487208097 cites W2030988632 @default.
- W1487208097 cites W2031458328 @default.
- W1487208097 cites W2032420355 @default.
- W1487208097 cites W2032997966 @default.
- W1487208097 cites W2033501845 @default.
- W1487208097 cites W2038899568 @default.
- W1487208097 cites W2039799635 @default.
- W1487208097 cites W2041186729 @default.
- W1487208097 cites W2041656047 @default.
- W1487208097 cites W2045680092 @default.
- W1487208097 cites W2049911601 @default.