Matches in SemOpenAlex for { <https://semopenalex.org/work/W1601137172> ?p ?o ?g. }
- W1601137172 endingPage "751" @default.
- W1601137172 startingPage "743" @default.
- W1601137172 abstract "Although advances in the management of children with congenital cholestasis have enabled many to survive into adulthood with their native livers, even the most common of these conditions remains rare in adult hepatology practice. Among four congenital cholestatic syndromes (biliary atresia, Alagille syndrome, Caroli disease and congenital hepatic fibrosis, and progressive familial intrahepatic cholestasis), the published data on outcomes of the syndromes into adulthood suggest that a spectrum of severity of liver disease can be expected, from cirrhosis (almost universal in adults with biliary atresia who have not required liver transplantation) to mild and subclinical (eg, in the previously undiagnosed affected parent of an infant with Alagille syndrome). Complications associated with portal hypertension and nutritional deficiencies are common, and other associated features of the cholestatic syndrome may require appropriate attention, such as congenital heart disease in Alagille syndrome. Indications for liver transplantation include synthetic failure, progressive encephalopathy, intractable pruritus, recurrent biliary sepsis and recurrent complications of portal hypertension. Improved understanding of biliary physiology will hopefully translate into improved therapy for children and adults with cholestasis." @default.
- W1601137172 created "2016-06-24" @default.
- W1601137172 creator A5030788392 @default.
- W1601137172 date "2007-01-01" @default.
- W1601137172 modified "2023-10-18" @default.
- W1601137172 title "Congenital Cholestatic Syndromes: What Happens When Children Grow Up?" @default.
- W1601137172 cites W127269753 @default.
- W1601137172 cites W1481423371 @default.
- W1601137172 cites W1828308889 @default.
- W1601137172 cites W1832864842 @default.
- W1601137172 cites W1964201802 @default.
- W1601137172 cites W1966640789 @default.
- W1601137172 cites W1967393185 @default.
- W1601137172 cites W1968224951 @default.
- W1601137172 cites W1970273067 @default.
- W1601137172 cites W1971139086 @default.
- W1601137172 cites W1971926367 @default.
- W1601137172 cites W1973032652 @default.
- W1601137172 cites W1973679514 @default.
- W1601137172 cites W1974185766 @default.
- W1601137172 cites W1984274163 @default.
- W1601137172 cites W1986155425 @default.
- W1601137172 cites W1994271325 @default.
- W1601137172 cites W1997436888 @default.
- W1601137172 cites W1998851511 @default.
- W1601137172 cites W2001443677 @default.
- W1601137172 cites W2005491023 @default.
- W1601137172 cites W2009084021 @default.
- W1601137172 cites W2011889164 @default.
- W1601137172 cites W2012165524 @default.
- W1601137172 cites W2019159019 @default.
- W1601137172 cites W2021568532 @default.
- W1601137172 cites W2022113921 @default.
- W1601137172 cites W2023037394 @default.
- W1601137172 cites W2026922615 @default.
- W1601137172 cites W2035142208 @default.
- W1601137172 cites W2035855390 @default.
- W1601137172 cites W2036048866 @default.
- W1601137172 cites W2036657452 @default.
- W1601137172 cites W2039442002 @default.
- W1601137172 cites W2043229986 @default.
- W1601137172 cites W2048990275 @default.
- W1601137172 cites W2049948540 @default.
- W1601137172 cites W2051822058 @default.
- W1601137172 cites W2052966532 @default.
- W1601137172 cites W2055630306 @default.
- W1601137172 cites W2055839262 @default.
- W1601137172 cites W2056578624 @default.
- W1601137172 cites W2057843157 @default.
- W1601137172 cites W2060241102 @default.
- W1601137172 cites W2061060689 @default.
- W1601137172 cites W2064287634 @default.
- W1601137172 cites W2064609358 @default.
- W1601137172 cites W2072862534 @default.
- W1601137172 cites W2087017664 @default.
- W1601137172 cites W2091712728 @default.
- W1601137172 cites W2095409521 @default.
- W1601137172 cites W2099158058 @default.
- W1601137172 cites W2101223514 @default.
- W1601137172 cites W2110225368 @default.
- W1601137172 cites W2112857398 @default.
- W1601137172 cites W2132797608 @default.
- W1601137172 cites W2134283151 @default.
- W1601137172 cites W2143436143 @default.
- W1601137172 cites W2157058568 @default.
- W1601137172 cites W2157244334 @default.
- W1601137172 cites W2157291177 @default.
- W1601137172 cites W2159029076 @default.
- W1601137172 cites W2159584165 @default.
- W1601137172 cites W2160635275 @default.
- W1601137172 cites W2162984856 @default.
- W1601137172 cites W2166252848 @default.
- W1601137172 cites W2171716651 @default.
- W1601137172 cites W2329906099 @default.
- W1601137172 cites W2996497172 @default.
- W1601137172 doi "https://doi.org/10.1155/2007/581247" @default.
- W1601137172 hasPubMedCentralId "https://www.ncbi.nlm.nih.gov/pmc/articles/2658590" @default.
- W1601137172 hasPubMedId "https://pubmed.ncbi.nlm.nih.gov/18026579" @default.
- W1601137172 hasPublicationYear "2007" @default.
- W1601137172 type Work @default.
- W1601137172 sameAs 1601137172 @default.
- W1601137172 citedByCount "23" @default.
- W1601137172 countsByYear W16011371722012 @default.
- W1601137172 countsByYear W16011371722013 @default.
- W1601137172 countsByYear W16011371722014 @default.
- W1601137172 countsByYear W16011371722015 @default.
- W1601137172 countsByYear W16011371722016 @default.
- W1601137172 countsByYear W16011371722017 @default.
- W1601137172 countsByYear W16011371722019 @default.
- W1601137172 countsByYear W16011371722022 @default.
- W1601137172 countsByYear W16011371722023 @default.
- W1601137172 crossrefType "journal-article" @default.
- W1601137172 hasAuthorship W1601137172A5030788392 @default.
- W1601137172 hasBestOaLocation W16011371721 @default.
- W1601137172 hasConcept C113280763 @default.
- W1601137172 hasConcept C126322002 @default.
- W1601137172 hasConcept C187212893 @default.
- W1601137172 hasConcept C2776366509 @default.