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- W164094626 abstract "The enteric nervous system (ENS) that forms along the entire length of the bowel is derived principally from neural crest cells (NCC) that have emigrated from the vagal level of the neural tube adjacent to somites 1–7. Normal ENS development during embryogenesis requires the completion of two key steps: first, the arrival and then entry of sufficient numbers of NCC into the foregut, and second, the survival, migration, proliferation, and then differentiation of NCC into ganglia. Defects in any of these processes causes an absence of ganglia along variable lengths of the bowel that underlies Hirschsprung disease (HSCR), the most common neurocristopathy in humans. Over a dozen different genes have been identified in HSCR patients, and the role(s) that they play in ENS development and disease are described in this chapter." @default.
- W164094626 created "2016-06-24" @default.
- W164094626 creator A5064180516 @default.
- W164094626 date "2014-01-01" @default.
- W164094626 modified "2023-09-25" @default.
- W164094626 title "Neural Crest Cells in Enteric Nervous System Development and Disease" @default.
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