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- W1794752720 abstract "A 37-year-old woman presented with left eye pain, headaches, and vision loss. MRI showed a left sphenoid mass, with optic nerve compression and proptosis (figure 1). The left eye had minimal reactivity to light, scleral erythema, and proptosis. A metastatic lesion or a lymphoma was suspected; however, pathology showed an epithelioid hemangioendothelioma (figure 2). There was no extracranial disease. Intracranial epithelioid hemangioendothelioma is rare, with around 40 reports. Thirty-two percent show local invasion, mortality is 15%, 24% recur, and 15% metastasize.1 It is associated with the WWTR1/CAMTA1 fusion protein.2 The treatment is surgery, with unclear roles for adjuvant therapy.1" @default.
- W1794752720 created "2016-06-24" @default.
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- W1794752720 date "2015-08-24" @default.
- W1794752720 modified "2023-09-25" @default.
- W1794752720 title "Intracranial epithelioid hemangioendothelioma causing subacute loss of vision" @default.
- W1794752720 cites W2080674605 @default.
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- W1794752720 doi "https://doi.org/10.1212/wnl.0000000000001873" @default.
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