Matches in SemOpenAlex for { <https://semopenalex.org/work/W1906921630> ?p ?o ?g. }
- W1906921630 abstract "Progressive myoclonus epilepsy of the Unverricht–Lundborg type is a rare disorder associated with mutations in gene encoding the cystatin B, an inhibitor of cysteine proteases. Cystatin B knockout mice share phenotype with human disease demonstrating similarly the myoclonic seizures, progressive ataxia and neuronal atrophy in hippocampus and cerebellum. We used liquid chromatographic and real time PCR techniques to determine whether glutamate and GABA content as well as vesicular glutamate transporter 1, vesicular GABA transporter 1 and glutamic acid decarboxylase (GAD65) gene expression levels are disturbed in mutant mice brain. We found the significant decrease in glutamate content and vesicular glutamate transporter 1 gene expression levels as well as the increase in GAD65 expression levels while the GABA transporter gene and GABA concentrations remain unchanged in" @default.
- W1906921630 created "2016-06-24" @default.
- W1906921630 creator A5011440112 @default.
- W1906921630 date "2007-08-21" @default.
- W1906921630 modified "2023-09-27" @default.
- W1906921630 title "The studies on cystatin B deficient mice: neurochemical and behavioural alterations in animal model of progressive myoclonus epilepsy of Unverricht–Lundborg type" @default.
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