Matches in SemOpenAlex for { <https://semopenalex.org/work/W19295813> ?p ?o ?g. }
- W19295813 endingPage "611" @default.
- W19295813 startingPage "585" @default.
- W19295813 abstract "Inherited disorders of platelet function are characterized by highly variable mucocutaneous bleeding manifestations. The platelet dysfunction arises by diverse mechanisms, including abnormalities in platelet membrane glycoproteins, granules and their contents, platelet signaling and secretion mechanisms: thromboxane production pathways and in platelet procoagulant activities. Platelet aggregation and secretion studies using platelet-rich plasma currently form the primary basis for the diagnosis of an inherited platelet dysfunction. In most such patients, the molecular and genetic mechanisms are unknown. Management of these patients needs to be individualized; therapeutic options include platelet transfusions, 1-desamino-8d-arginine vasopressin (DDAVP), recombinant factor VIIa, and antifibrinolytic agents." @default.
- W19295813 created "2016-06-24" @default.
- W19295813 creator A5061115846 @default.
- W19295813 date "2013-06-01" @default.
- W19295813 modified "2023-09-27" @default.
- W19295813 title "Inherited Platelet Function Disorders" @default.
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