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- W1970015257 abstract "Pemphigus vulgaris (PV) is a life-threatening blistering autoimmune disease of the skin and mucous membranes characterized by autoantibodies (autoAbs) against desmoglein 3 (Dsg3), a desmosomal adhesion protein expressed on the surface of epidermal keratinocytes. Loss of adhesion between epidermal keratinocytes leads to extensive blisters and painful erosions of mucous membranes and skin (Fig. 1). Recently developed in vitro and in vivo models of PV contributed significantly to a better understanding of its pathogenesis including the pathogenic role of autoAbs and the regulation of autoreactive B- and T-cell activation." @default.
- W1970015257 created "2016-06-24" @default.
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- W1970015257 date "2006-03-01" @default.
- W1970015257 modified "2023-09-25" @default.
- W1970015257 title "Models of pemphigus vulgaris" @default.
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- W1970015257 doi "https://doi.org/10.1016/j.ddmod.2006.03.009" @default.
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