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- W1971567502 abstract "Resumen La neurofibromatosis tipo 1 aumenta el riesgo de incidencia de padecer cierto tipo de canceres, en particular con el schwannoma maligno o neurofibrosarcoma. Presentamos el caso de una paciente de (61) anos de edad con antecedente de enfermedad de Von Recklinghausen, intervenida hace (30) anos de schwannomas cervicales y oftalmicos. Evolutivamente, presenta clinica de compresion de raices nerviosas (L3-4) izquierdas evidenciandose una masa retroperitoneal. Se diagnostica de schwanoma epitelial maligno mediante biopsia y se indica intervencion quirurgica, practicandose reseccion en bloque de la masa. La evolucion posquirurgica fue favorable; al ano de la intervencion la paciente presenta un deficit motor residual en la extension, y sensitivo en la region anterolateral de la extremidad inferior izquierda. El tratamiento de eleccion del schwanoma maligno es la cirugia, dado que proporciona supervivencias prolongadas." @default.
- W1971567502 created "2016-06-24" @default.
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- W1971567502 date "2003-01-01" @default.
- W1971567502 modified "2023-10-17" @default.
- W1971567502 title "Schwannoma retroperitoneal maligno asociado a neurofibromatosis" @default.
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- W1971567502 doi "https://doi.org/10.1016/s0009-739x(03)72134-4" @default.
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