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- W1973673075 endingPage "45" @default.
- W1973673075 startingPage "33" @default.
- W1973673075 abstract "Prion diseases form a group of neurodegenerative disorders with the unique feature of being transmissible. These diseases involve a pathogenic protein, called PrPSc for the scrapie isoform of the cellular prion protein (PrPC) which is an abnormally-folded counterpart of PrPC. Many questions remain unresolved concerning the function of PrPC and the mechanisms underlying prion replication, transmission and neurodegeneration. PrPC is a glycosyl-phosphatidylinositol-anchored glycoprotein expressed at the cell surface of neurons and other cell types. PrPC may be present as distinct isoforms depending on proteolytic processing (full length and truncated), topology(GPI-anchored, transmembrane or soluble) and glycosylation (non- mono- and di-glycosylated). The present review focuses on the implications of PrPC glycosylation as to the function of the normal protein, the cellular pathways of conversion into PrPSc, the diversity of prion strains and the related selective neuronal targeting." @default.
- W1973673075 created "2016-06-24" @default.
- W1973673075 creator A5083174961 @default.
- W1973673075 date "2003-02-01" @default.
- W1973673075 modified "2023-10-15" @default.
- W1973673075 title "Evolving views in prion glycosylation: functional and pathological implications" @default.
- W1973673075 cites W1455622067 @default.
- W1973673075 cites W1480545630 @default.
- W1973673075 cites W1483315850 @default.
- W1973673075 cites W1501494207 @default.
- W1973673075 cites W1502642270 @default.
- W1973673075 cites W1504267511 @default.
- W1973673075 cites W1510907115 @default.
- W1973673075 cites W1513744325 @default.
- W1973673075 cites W1525316969 @default.
- W1973673075 cites W1540278447 @default.
- W1973673075 cites W1543396712 @default.
- W1973673075 cites W1554099072 @default.
- W1973673075 cites W1554709620 @default.
- W1973673075 cites W1557182452 @default.
- W1973673075 cites W1559478955 @default.
- W1973673075 cites W1562167215 @default.
- W1973673075 cites W1583440911 @default.
- W1973673075 cites W1604226917 @default.
- W1973673075 cites W1619710608 @default.
- W1973673075 cites W1644854647 @default.
- W1973673075 cites W1704732331 @default.
- W1973673075 cites W1784563469 @default.
- W1973673075 cites W1799441155 @default.
- W1973673075 cites W187449250 @default.
- W1973673075 cites W187964537 @default.
- W1973673075 cites W1879803811 @default.
- W1973673075 cites W1938969372 @default.
- W1973673075 cites W1964241324 @default.
- W1973673075 cites W1964249554 @default.
- W1973673075 cites W1964906994 @default.
- W1973673075 cites W1965378784 @default.
- W1973673075 cites W1970921752 @default.
- W1973673075 cites W1971835950 @default.
- W1973673075 cites W1974443289 @default.
- W1973673075 cites W1975109489 @default.
- W1973673075 cites W1976601347 @default.
- W1973673075 cites W1978523429 @default.
- W1973673075 cites W1979041460 @default.
- W1973673075 cites W1983292653 @default.
- W1973673075 cites W1986350331 @default.
- W1973673075 cites W1986735189 @default.
- W1973673075 cites W1986896358 @default.
- W1973673075 cites W1988722496 @default.
- W1973673075 cites W1989081602 @default.
- W1973673075 cites W1989400359 @default.
- W1973673075 cites W1989989032 @default.
- W1973673075 cites W1990290617 @default.
- W1973673075 cites W1990496336 @default.
- W1973673075 cites W1990623935 @default.
- W1973673075 cites W1991211881 @default.
- W1973673075 cites W1992380356 @default.
- W1973673075 cites W1994172525 @default.
- W1973673075 cites W1995455102 @default.
- W1973673075 cites W1995673366 @default.
- W1973673075 cites W1997725693 @default.
- W1973673075 cites W1999705715 @default.
- W1973673075 cites W2000319181 @default.
- W1973673075 cites W2001536880 @default.
- W1973673075 cites W2004093049 @default.
- W1973673075 cites W2008789887 @default.
- W1973673075 cites W2010184287 @default.
- W1973673075 cites W2010238780 @default.
- W1973673075 cites W2010745676 @default.
- W1973673075 cites W2013198566 @default.
- W1973673075 cites W2015350567 @default.
- W1973673075 cites W2015774470 @default.
- W1973673075 cites W2020258831 @default.
- W1973673075 cites W2021505439 @default.
- W1973673075 cites W2021760309 @default.
- W1973673075 cites W2021800656 @default.
- W1973673075 cites W2022614447 @default.
- W1973673075 cites W2023529808 @default.
- W1973673075 cites W2027022625 @default.
- W1973673075 cites W2032604948 @default.
- W1973673075 cites W2032860676 @default.
- W1973673075 cites W2033367680 @default.
- W1973673075 cites W2034120336 @default.
- W1973673075 cites W2034797921 @default.
- W1973673075 cites W2035144845 @default.
- W1973673075 cites W2035737002 @default.
- W1973673075 cites W2037762998 @default.
- W1973673075 cites W2038887966 @default.
- W1973673075 cites W2042203193 @default.
- W1973673075 cites W2043492740 @default.
- W1973673075 cites W2043943109 @default.
- W1973673075 cites W2044666532 @default.
- W1973673075 cites W2046487370 @default.
- W1973673075 cites W2049055716 @default.
- W1973673075 cites W2052901299 @default.
- W1973673075 cites W2053400919 @default.
- W1973673075 cites W2053636966 @default.
- W1973673075 cites W2055188598 @default.