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- W1976721694 abstract "La β-thalassémie est une hémoglobinopathie génétique. Elle est parfois associée à une hypercoagulabilité, une altération de l’arbre vasculaire et des accidents thromboemboliques. La survenue d’hémorragie sous-arachnoïdienne spontanée dans cette affection est plus rare. Cette complication est rapportée lors du post-partum, chez une femme de 27 ans atteinte de β-thalassémie majeure. Les examens neuroradiologiques révélaient la présence d’anomalies vasculaires multiples (occlusion carotidienne intracrânienne, micro-anévrismes carotidiens, artères perforantes et corticales anormalement développées). Ces aspects fondent l’originalité de cette observation. β-thalassemia is a genetic hemoglobinopathy, which can cause hypercoagulability, vessel wall damages and thromboembolic events. Spontaneous subarachnoidal hemorrhages are not commonly described in this affection. We report subarachnoidal hemorrhage, observed during the post-partum period in a 27-year-old woman suffering from β-thalassemia major. Brain MRI revealed complex vascular abnormalities: intracranial carotid occlusion, carotid micro-aneurisms, abnormally developed deep perforators and cortical arteries." @default.
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- W1976721694 date "2013-03-01" @default.
- W1976721694 modified "2023-09-25" @default.
- W1976721694 title "Hémorragie sous-arachnoïdienne et anomalies vasculaires cérébrales multiples au cours d’une β-thalassémie majeure" @default.
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- W1976721694 doi "https://doi.org/10.1016/j.neurol.2012.09.015" @default.
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