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- W1981069139 abstract "Juvenile dermatomyositis (JDM) is a rare, potentially life-threatening systemic autoimmune disease primarily affecting muscle and skin. Recent advances in the recognition, standardised assessment and treatment of JDM have been greatly facilitated by large collaborative research networks. Through these networks, a number of immunogenetic risk factors have now been defined, as well as a number of potential pathways identified in the aetio-pathogenesis of JDM. Myositis-associated and myositis-specific autoantibodies are helping to sub-phenotype JDM, defined by clinical features, outcomes and immunogenetic risk factors. Partially validated tools to assess disease activity and damage have assisted in standardising outcomes. Aggressive treatment approaches, including multiple initial therapies, as well as new drugs and biological therapies for refractory disease, offer promise of improved outcomes and less corticosteroid-related toxicity." @default.
- W1981069139 created "2016-06-24" @default.
- W1981069139 creator A5037338479 @default.
- W1981069139 creator A5040273759 @default.
- W1981069139 date "2009-10-01" @default.
- W1981069139 modified "2023-10-17" @default.
- W1981069139 title "Juvenile dermatomyositis: new developments in pathogenesis, assessment and treatment" @default.
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- W1981069139 doi "https://doi.org/10.1016/j.berh.2009.07.007" @default.
- W1981069139 hasPubMedCentralId "https://www.ncbi.nlm.nih.gov/pmc/articles/2774891" @default.
- W1981069139 hasPubMedId "https://pubmed.ncbi.nlm.nih.gov/19853831" @default.