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- W1987151903 abstract "Fat-soluble vitamin status was assessed in 36 infants diagnosed with cystic fibrosis by newborn screening in the Colorado Program. At the time of diagnosis of cystic fibrosis, 36% of infants were hypoalbuminemic, 21% had vitamin A deficiency, 35% had vitamin D deficiency, and 38% had vitamin E deficiency. None had vitamin K deficiency. Supplementation with pancreatic enzymes, a multiple vitamin preparation, and additional vitamin E was associated with normalization of serum albumin, retinol, and 25-hydroxyvitamin D and negative PIVKA testing at age 6 and 12 months. Several patients remained vitamin E deficient, but this was felt to be due to poor compliance. Biochemical evidence of fat-soluble vitamin deficiency is common before age 3 months in infants with CF and responds to supplementation in the first year of life. Pediatr Pulmonol. 1991; Supp 7: 52–55." @default.
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- W1987151903 date "1991-01-01" @default.
- W1987151903 modified "2023-10-18" @default.
- W1987151903 title "Fat-soluble vitamins in infants identified by cystic fibrosis newborn screening" @default.
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- W1987151903 doi "https://doi.org/10.1002/ppul.1950110711" @default.
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