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- W1987533749 endingPage "189" @default.
- W1987533749 startingPage "173" @default.
- W1987533749 abstract "The expression, processing, transport and activities of both coding and non-coding RNAs play critical roles in normal neuronal function and differentiation. Over the past decade, these same pathways have come under scrutiny as potential contributors to neurodegenerative disease. Here we focus broadly on the roles of RNA and RNA processing in neurodegeneration. We first discuss a set of “RNAopathies”, where non-coding repeat expansions drive pathogenesis through a surprisingly diverse set of mechanisms. We next explore an emerging class of “RNA binding proteinopathies” where redistribution and aggregation of the RNA binding proteins TDP-43 or FUS contribute to a potentially broad range of neurodegenerative disorders. Lastly, we delve into the potential contributions of alterations in both short and long non-coding RNAs to neurodegenerative illness." @default.
- W1987533749 created "2016-06-24" @default.
- W1987533749 creator A5001583322 @default.
- W1987533749 creator A5052365625 @default.
- W1987533749 date "2012-05-01" @default.
- W1987533749 modified "2023-09-25" @default.
- W1987533749 title "Neurodegeneration the RNA way" @default.
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