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- W1987698749 abstract "Le purpura rhumatoïde est une vascularite habituellement d'évolution spontanément favorable. Dans 70% des cas, les patients présentent des troubles digestifs, pouvant évoluer jusqu'à l'invagination ou la perforation intestinale. Il n'existe pas de preuve de l'efficacité d'un traitement dans les formes compliquées de purpura rhumatoïde. Les corticoïdes améliorent les douleurs abdominales mais ils n'ont pas d'effet sur l'atteinte rénale ni sur la prévention des récidives. Les immunoglobulines intraveineuses ont montré une efficacité dans quelques cas avec atteinte abdominale récidivante ou avec atteinte rénale progressive. Nous rapportons le cas d'un patient de 19 ans présentant une forme digestive sévère et rénale débutante de maladie d'Henoch-Schönlein, rapidement améliorée et de façon durable par des immunoglobulines intraveineuses administrées pendant 48 heures.Henoch-Schönlein purpura is a vasculitis usually with a benign course. Abdominal symptoms occur in 70% of cases, with possible intussusception or intestinal perforation. There is no clear evidence of the efficacy of a treatment in complicated cases of Henoch-Schönlein purpura. Corticosteroids improve abdominal pain but they do not have any effect on renal involvement or prevention of relapses. Intravenous immunoglobulins have been efficient in some cases with recurrent abdominal symptoms or progressive renal lesions. We report the case of a 19-year-old patient with severe abdominal involvement and early renal manifestations of Henoch-Schönlein disease, rapid and sustained improvement was obtained by intravenous immunoglobulins given during 48 hours." @default.
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- W1987698749 date "2002-12-01" @default.
- W1987698749 modified "2023-10-14" @default.
- W1987698749 title "Vascularite appendiculaire révélant un purpura rhumatoïde" @default.
- W1987698749 doi "https://doi.org/10.1016/s0248-8663(02)80529-x" @default.
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