Matches in SemOpenAlex for { <https://semopenalex.org/work/W1990956835> ?p ?o ?g. }
- W1990956835 endingPage "85" @default.
- W1990956835 startingPage "71" @default.
- W1990956835 abstract "This is the third article related to a review of the literature based on data from national cystic fibrosis (CF) patient registries up to June 2008 and covering a total of 115 published studies. It focuses on several topics: CF incidence, genotype/phenotype correlation, microbiology, pregnancy/paternity, clinical complications, lung transplantation, and others.Seventy seven papers meeting the inclusion criteria were found to be related to the topics listed above. Another seven studies, already evaluated in previous papers of this series, were recalled for specific topics.Incidence is described by several studies, results being quite different from one country to another and quite inhomogeneous among regions within the same country. Studies on genetics address the genotype/phenotype correlation and look for a predictive value of CFTR mutations in terms of clinical outcome, with controversial results. Papers on microbiology describe the clinical relevance of different pathogens and their role in the progress of CF lung disease. A few articles give information on the features of CF women undergoing a pregnancy and try to identify the ones associated with a better outcome. Studies on clinical complications discuss prevalence and the role of haemoptysis, pneumothorax, CF related diabetes, ABPA and cancer. Papers on lung transplantation focus on models able to improve the selection criteria for transplantation candidates and the factors linked to post transplantation survival. Finally, several studies deal with a number of interesting topics related to CF epidemiology: clinical trial methodology, quality of care comparison among countries and centers, relationship between diagnosis and age/gender, and evaluation of pharmacological therapy.On the whole, CF Registries have already contributed to important advances in the knowledge of the natural history of CF, establishing the foundations for future improvement in CF research and care." @default.
- W1990956835 created "2016-06-24" @default.
- W1990956835 creator A5002549022 @default.
- W1990956835 creator A5006141192 @default.
- W1990956835 creator A5006241407 @default.
- W1990956835 creator A5007016195 @default.
- W1990956835 creator A5007867642 @default.
- W1990956835 creator A5035013267 @default.
- W1990956835 creator A5037732667 @default.
- W1990956835 creator A5044258108 @default.
- W1990956835 creator A5063502705 @default.
- W1990956835 creator A5079973168 @default.
- W1990956835 creator A5086480079 @default.
- W1990956835 creator A5088711997 @default.
- W1990956835 date "2011-03-01" @default.
- W1990956835 modified "2023-09-27" @default.
- W1990956835 title "An overview of international literature from cystic fibrosis registries. Part 3. Disease incidence, genotype/phenotype correlation, microbiology, pregnancy, clinical complications, lung transplantation, and miscellanea" @default.
- W1990956835 cites W1966242444 @default.
- W1990956835 cites W1966937543 @default.
- W1990956835 cites W1967064450 @default.
- W1990956835 cites W1971558827 @default.
- W1990956835 cites W1978991565 @default.
- W1990956835 cites W1979046027 @default.
- W1990956835 cites W1980106563 @default.
- W1990956835 cites W1983068671 @default.
- W1990956835 cites W1984880642 @default.
- W1990956835 cites W1989143325 @default.
- W1990956835 cites W1990336663 @default.
- W1990956835 cites W1993616165 @default.
- W1990956835 cites W1996587392 @default.
- W1990956835 cites W2000825443 @default.
- W1990956835 cites W2002352467 @default.
- W1990956835 cites W2009330310 @default.
- W1990956835 cites W2009368678 @default.
- W1990956835 cites W2011048239 @default.
- W1990956835 cites W2016713016 @default.
- W1990956835 cites W2018403515 @default.
- W1990956835 cites W2018466867 @default.
- W1990956835 cites W2022166103 @default.
- W1990956835 cites W2023192638 @default.
- W1990956835 cites W2032406037 @default.
- W1990956835 cites W2033669363 @default.
- W1990956835 cites W2034127068 @default.
- W1990956835 cites W2037008685 @default.
- W1990956835 cites W2038652410 @default.
- W1990956835 cites W2039081605 @default.
- W1990956835 cites W2039599894 @default.
- W1990956835 cites W2041431539 @default.
- W1990956835 cites W2042259052 @default.
- W1990956835 cites W2045660987 @default.
- W1990956835 cites W2051327498 @default.
- W1990956835 cites W2051556779 @default.
- W1990956835 cites W2053220154 @default.
- W1990956835 cites W2054587742 @default.
- W1990956835 cites W2056538792 @default.
- W1990956835 cites W2058460570 @default.
- W1990956835 cites W2066416876 @default.
- W1990956835 cites W2067404409 @default.
- W1990956835 cites W2070097998 @default.
- W1990956835 cites W2071883313 @default.
- W1990956835 cites W2073009316 @default.
- W1990956835 cites W2078685101 @default.
- W1990956835 cites W2079147446 @default.
- W1990956835 cites W2079477694 @default.
- W1990956835 cites W2081002142 @default.
- W1990956835 cites W2082510149 @default.
- W1990956835 cites W2086189756 @default.
- W1990956835 cites W2086235445 @default.
- W1990956835 cites W2088679601 @default.
- W1990956835 cites W2090401303 @default.
- W1990956835 cites W2092048896 @default.
- W1990956835 cites W2096963724 @default.
- W1990956835 cites W2100523177 @default.
- W1990956835 cites W2103193749 @default.
- W1990956835 cites W2103879666 @default.
- W1990956835 cites W2109530959 @default.
- W1990956835 cites W2111878868 @default.
- W1990956835 cites W2113774097 @default.
- W1990956835 cites W2114386901 @default.
- W1990956835 cites W2114397632 @default.
- W1990956835 cites W2119039665 @default.
- W1990956835 cites W2119858224 @default.
- W1990956835 cites W2121146879 @default.
- W1990956835 cites W2121500558 @default.
- W1990956835 cites W2127339866 @default.
- W1990956835 cites W2133312232 @default.
- W1990956835 cites W2136496779 @default.
- W1990956835 cites W2138822434 @default.
- W1990956835 cites W2140119907 @default.
- W1990956835 cites W2141642277 @default.
- W1990956835 cites W2144152902 @default.
- W1990956835 cites W2144947606 @default.
- W1990956835 cites W2147695950 @default.
- W1990956835 cites W2148537390 @default.
- W1990956835 cites W2150396086 @default.
- W1990956835 cites W2150915979 @default.
- W1990956835 cites W2151135498 @default.
- W1990956835 cites W2152397772 @default.