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- W1992319326 abstract "Les aortites sont principalement retrouvées au cours des maladies inflammatoires comme l’artérite de Takayasu, l’artérite à cellules géantes ou la maladie de Behçet. Dans certains cas, l’aortite est dite idiopathique lorsqu’aucune de ces causes n’est retrouvée. Certains diagnostics différentiels doivent cependant être évoqués car leur prise en charge est bien différente. En premier lieu, il faut éliminer une cause infectieuse de l’aortite car leur rapidité d’évolution et leur pronostic à court terme en font une urgence thérapeutique. Ensuite, des diagnostics différentiels plus rares sont à connaître comme la fibrose rétropéritonéale le plus souvent idiopathique, mais parfois associée à une néoplasie ou une hémopathie. La maladie associée aux IgG4, la maladie d’Erdheim-Chester et l’anévrisme inflammatoire athéromateux sont d’autres diagnostics différentiels à évoquer devant une aortite inflammatoire afin d’adapter au mieux la prise en charge de ces patients.Aortitis are mainly described in inflammatory disorders such as Takayasu arteritis, giant cell arteritis or Behçet's disease. Aortitis is sometimes qualified as idiopathic. However, differential diagnoses must be searched since they need specific interventions. Infectious aortitis should be ruled out first as its rapid evolution and short-term poor prognosis makes it a therapeutic emergency. Furthermore, rarer differential diagnoses should be known as they require specific care that might sometimes differ from the treatment of inflammatory aortitis, such as retroperitoneal fibrosis mostly idiopathic but also secondary to neoplasia or malignant hemopathies. IgG4 related disease, Erdheim-Chester disease and inflammatory abdominal aortic aneurysm due to atherosclerosis are other differential diagnoses to mention in the presence of aortitis in order to adapt patients’ care consequently." @default.
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- W1992319326 date "1997-01-01" @default.
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- W1992319326 title "Polyangéite microscopique: manifestations cliniques, signes biologiques et pronostiques chez 89 patients" @default.
- W1992319326 doi "https://doi.org/10.1016/s0248-8663(97)80236-6" @default.
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