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- W1993916257 endingPage "729" @default.
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- W1993916257 abstract "Extrahepatic biliary atresia (EHBA), an inflammatory sclerosing cholangiopathy, is the leading indication for liver transplantation in children. The cause is still unknown, although possible infectious, genetic, and immunologic etiologies have received much recent focus. These theories are often dependent on each other for secondary or coexisting mechanisms. Concern for EHBA is raised by a cholestatic infant, but the differential diagnosis is large and the path to diagnosis remains varied. Current treatment is surgical with an overall survival rate of approximately 90%. The goals of this article are to review the important clinical aspects of EHBA and to highlight some of the more recent scientific and clinical developments contributing to our understanding of this condition." @default.
- W1993916257 created "2016-06-24" @default.
- W1993916257 creator A5056406094 @default.
- W1993916257 creator A5060734873 @default.
- W1993916257 date "2008-07-01" @default.
- W1993916257 modified "2023-09-30" @default.
- W1993916257 title "Biliary Atresia" @default.
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