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- W1996504852 endingPage "184" @default.
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- W1996504852 abstract "MBL-deficiency is a commonly occurring deficiency of the innate immune system, affecting a substantial part of the population and has been extensively studied. MBL appears to function as a disease modifier. The role of MBL in different conditions is context-dependent. Many clinical studies show conflicting results, which can be partially explained by different definitions of MBL-deficiency, including phenotype- and genotype-based approaches. In this review we give an overview of literature of MBL, its role in different pathologies, diseases and patient populations. We review MBL replacement studies, and discuss the potential of MBL substitution therapy. We finally suggest that new MBL substitution trials should be conducted within a predefined patient population. MBL-deficiency should be based on serum levels and confirmed by genotyping." @default.
- W1996504852 created "2016-06-24" @default.
- W1996504852 creator A5001479406 @default.
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- W1996504852 creator A5014330443 @default.
- W1996504852 creator A5046590750 @default.
- W1996504852 date "2014-10-01" @default.
- W1996504852 modified "2023-09-30" @default.
- W1996504852 title "Restoration of MBL-deficiency: Redefining the safety, efficacy and viability of MBL-substitution therapy" @default.
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