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- W2000831769 abstract "Le syndrome de Miller-Fisher (SMF) d’étiologie post-infectieuse auto-immune est une association rare caractérisée par une ataxie, une ophtalmoplégie et une aréflexie généralisée qui se rapproche du syndrome de Guillain et Barré (SGB). Les formes récidivantes de SMF sont exceptionnellement rapportées dans la littérature. Nous rapportons le cas d’une patiente âgée de 54 ans ayant présenté un SMF à rechute, avec deux épisodes survenus à 19 ans d’intervalle. Les deux épisodes avaient une gravité clinique différente, mais un bon pronostic évolutif. Le premier épisode était précédé d’une affection virale avec signes digestifs et le second avec signes respiratoires. Lors du deuxième épisode, l’étude électrophysiologique mit en évidence des anomalies sensitives très limitées aux territoires des nerfs médians. L’étude du liquide céphalo-rachidien était normale ainsi que l’IRM cérébrale. Les anticorps anti-GQ1b étaient fortement positifs, les anticorps anti-GM1 et GM2 faiblement positifs et la sérologie Campylobacter jejuni restait négative. Ce cas souligne la variété des manifestations cliniques et paracliniques des SMF sporadiques ou récurrents. Les rapports nosologiques entre le SGB, le SMF et l’encéphalite de Bickerstaff sont discutés. Miller-Fisher syndrome (MFS) is a rare auto-immune post-infectious syndrome, characterized by an ataxia, an ophthalmoplegia and a generelized areflexia. It is considered as a clinical variant of Guillain-Barré syndrome (GBS). MFS is correlated with the presence of anti-GQ1b antibodies, elevated cerebrospinal fluid (CSF) protein levels, presence of mostly sensitive electrophysiological abnormalities and for some authors central involvement with increased signal intensity of brainstem and cerebellum on MRI. Recurrent MFS is extremely rare with only 21 ases since the first description in 1970. A 54-year-old women presented MFS with two episodes in 19 years. Clinically, the first episode was a “classical” MFS, and the second an extensive MFS with tetraparesis and respiratory failure. CSF protein levels and cerebral MRI were normal. Anti-GQ1b antibodies were strongly positive and anti-GM1, anti-GM2 antibodies were slightly positive, campylobacter jejuni serology was negative. Electromyography showed isolated sensory abnormalities in median nerves territory. We report a new case of recurrent MFS with unusual clinical, biological and electrophysiological features." @default.
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- W2000831769 date "2005-09-01" @default.
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- W2000831769 title "Syndrome de Miller-Fisher récidivant" @default.
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- W2000831769 doi "https://doi.org/10.1016/s0035-3787(05)85146-x" @default.
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