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- W2003302088 abstract "Summary. Functional deficiency or absence of the human von Willebrand factor (VWF)-cleaving protease (VWF-cp), recently termed ADAMTS13, has been shown to cause acquired and congenital thrombotic thrombocytopenic purpura (TTP), respectively. As a first step towards developing a small animal model of TTP, we have cloned the complete (non-truncated) murine Adamts13 gene from BALB/c mice liver poly A+ mRNA. Murine ADAMTS13 is a 1426-amino-acid protein with a high homology and similar structural organization to the human ortholog. Transient expression of the murine Adamts13 cDNA in HEK 293 cells yielded a protein with a molecular weight of approximately 180 kDa which degraded recombinant murine VWF (rVWF) in a dose-dependent manner. The cleavage products of murine rVWF had the expected size of 140 and 170 kDa. Murine ADAMTS13 was inhibited by EDTA and the plasma from a TTP patient." @default.
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- W2003302088 date "2005-05-01" @default.
- W2003302088 modified "2023-10-03" @default.
- W2003302088 title "Cloning, expression and functional characterization of the full‐length murine ADAMTS13" @default.
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- W2003302088 doi "https://doi.org/10.1111/j.1538-7836.2005.01246.x" @default.
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