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- W200681004 abstract "Henoch-Schönlein purpura is a systemic vasculitis of the small vessels characterized by perivascular leucocyte infiltrates. It is an immunoglobulin A-related immune complex-mediated disease involving the skin, the joints and the gastrointestinal system. Renal disease may sometimes be associated to these clinical manifestations. Prevalence of the nephritis is highly variable, depending on the series. More rarely, other organs such as the lungs, the heart or the nervous system may be involved. The clinical diagnosis is confirmed by histopathology of the skin (leukocytoclastic vasculitis) and kidney (endo-capillary proliferative glomerulonephritis), showing IgA deposits in these tissues. Short-term prognosis depends on the severity of digestive involvement, but long-term prognosis depends on the renal disease. Recent publications of pediatric and adult series show that the chronic renal failure may progress, sometimes more than ten years after the initial flare. Treatment is usually supportive. The benefit of more specific treatments (corticosteroids or immunosuppressive drugs) in severe visceral forms (usually abdominal or kidney) has not yet been established." @default.
- W200681004 created "2016-06-24" @default.
- W200681004 creator A5011274752 @default.
- W200681004 creator A5070287120 @default.
- W200681004 date "2014-06-01" @default.
- W200681004 modified "2023-10-17" @default.
- W200681004 title "Purpura rhumatoïde de l’adulte" @default.
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- W200681004 doi "https://doi.org/10.1016/j.revmed.2013.12.004" @default.
- W200681004 hasPubMedId "https://pubmed.ncbi.nlm.nih.gov/24657040" @default.
- W200681004 hasPublicationYear "2014" @default.
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