FRINK Linked Data Fragments server

Matches in SemOpenAlex for { <https://semopenalex.org/work/W2007129218> ?p ?o ?g. }

• W2007129218 endingPage "718" @default.
• W2007129218 startingPage "712" @default.
• W2007129218 abstract "Epidermolysis bullosa acquisita is a rare autoimmune disease, characterized by the synthesis of anti-collagen VII autoantibodies, the main component of hemidesmosome anchoring fibrils. The antigen-antibody binding elicits a complex inflammatory response, which culminates in the loss of dermo-epidermal adhesion of the skin and/or mucous membranes. Skin fragility with bullae, erosions, and milia in areas of trauma characterizes the mechanobullous form of the disease. In the inflammatory form of epidermolysis bullosa acquisita, urticarial inflammatory plaques with tense bullae, similar to bullous pemphigoid, or mucosal lesions can determine permanent scars and loss of functionality in the ocular, oral, esophageal, and urogenital regions. Due to the similarity of the clinical findings of epidermolysis bullosa acquisita with other diseases of the pemphigoid group and with porphyria cutanea tarda, the diagnosis is currently confirmed mainly based on the clinical correlation with histopathological findings (pauci-inflammatory subepidermal cleavage or with a neutrophilic infiltrate) and the demonstration of the presence of anti-collagen VII IgG in situ by direct immunofluorescence, or circulating anti-collagen VII IgG through indirect immunofluorescence and/or ELISA. There is no specific therapy for epidermolysis bullosa acquisita and the response to treatment is variable, usually with complete remission in children and a worse prognosis in adults with mucosal involvement. Systemic corticosteroids and immunomodulators (colchicine and dapsone) are alternatives for the treatment of mild forms of the disease, while severe forms require the use of corticosteroid therapy associated with immunosuppressants, intravenous immunoglobulin, and rituximab." @default.
• W2007129218 created "2016-06-24" @default.
• W2007129218 creator A5007855326 @default.
• W2007129218 creator A5027358797 @default.
• W2007129218 creator A5061514009 @default.
• W2007129218 creator A5065412207 @default.
• W2007129218 date "2001-11-01" @default.
• W2007129218 modified "2023-10-11" @default.
• W2007129218 title "Epidermolysis bullosa acquisita: update and review" @default.
• W2007129218 cites W1555229969 @default.
• W2007129218 cites W1967673016 @default.
• W2007129218 cites W1968008410 @default.
• W2007129218 cites W1968054341 @default.
• W2007129218 cites W1969239138 @default.
• W2007129218 cites W1971103686 @default.
• W2007129218 cites W1971831505 @default.
• W2007129218 cites W1977330416 @default.
• W2007129218 cites W1978669521 @default.
• W2007129218 cites W1979526481 @default.
• W2007129218 cites W1987619880 @default.
• W2007129218 cites W1990364618 @default.
• W2007129218 cites W1996425946 @default.
• W2007129218 cites W1997232609 @default.
• W2007129218 cites W1998584863 @default.
• W2007129218 cites W2000805297 @default.
• W2007129218 cites W2001205644 @default.
• W2007129218 cites W2001388818 @default.
• W2007129218 cites W2002023142 @default.
• W2007129218 cites W2013710029 @default.
• W2007129218 cites W2013863167 @default.
• W2007129218 cites W2024117150 @default.
• W2007129218 cites W2026129217 @default.
• W2007129218 cites W2026232580 @default.
• W2007129218 cites W2030785873 @default.
• W2007129218 cites W2035516919 @default.
• W2007129218 cites W2036730964 @default.
• W2007129218 cites W2037340555 @default.
• W2007129218 cites W2039739172 @default.
• W2007129218 cites W2044945049 @default.
• W2007129218 cites W2066026653 @default.
• W2007129218 cites W2067756121 @default.
• W2007129218 cites W2068021720 @default.
• W2007129218 cites W2070870690 @default.
• W2007129218 cites W2073867916 @default.
• W2007129218 cites W2082595087 @default.
• W2007129218 cites W2084157979 @default.
• W2007129218 cites W2086077250 @default.
• W2007129218 cites W2093527352 @default.
• W2007129218 cites W2094487977 @default.
• W2007129218 cites W2098502510 @default.
• W2007129218 cites W2098826532 @default.
• W2007129218 cites W2099936474 @default.
• W2007129218 cites W2127704761 @default.
• W2007129218 cites W2139860679 @default.
• W2007129218 cites W2142275262 @default.
• W2007129218 cites W2150388224 @default.
• W2007129218 cites W2157413892 @default.
• W2007129218 cites W2165523973 @default.
• W2007129218 cites W2313977109 @default.
• W2007129218 cites W4232815545 @default.
• W2007129218 cites W4237346858 @default.
• W2007129218 cites W4240205133 @default.
• W2007129218 cites W4241122629 @default.
• W2007129218 cites W4242317192 @default.
• W2007129218 cites W4244206589 @default.
• W2007129218 cites W4253013084 @default.
• W2007129218 cites W4253472764 @default.
• W2007129218 cites W52469116 @default.
• W2007129218 doi "https://doi.org/10.1016/s0738-081x(00)00186-3" @default.
• W2007129218 hasPubMedId "https://pubmed.ncbi.nlm.nih.gov/11705680" @default.
• W2007129218 hasPublicationYear "2001" @default.
• W2007129218 type Work @default.
• W2007129218 sameAs 2007129218 @default.
• W2007129218 citedByCount "52" @default.
• W2007129218 countsByYear W20071292182012 @default.
• W2007129218 countsByYear W20071292182013 @default.
• W2007129218 countsByYear W20071292182014 @default.
• W2007129218 countsByYear W20071292182016 @default.
• W2007129218 countsByYear W20071292182017 @default.
• W2007129218 countsByYear W20071292182018 @default.
• W2007129218 countsByYear W20071292182019 @default.
• W2007129218 countsByYear W20071292182022 @default.
• W2007129218 crossrefType "journal-article" @default.
• W2007129218 hasAuthorship W2007129218A5007855326 @default.
• W2007129218 hasAuthorship W2007129218A5027358797 @default.
• W2007129218 hasAuthorship W2007129218A5061514009 @default.
• W2007129218 hasAuthorship W2007129218A5065412207 @default.
• W2007129218 hasConcept C142724271 @default.
• W2007129218 hasConcept C159654299 @default.
• W2007129218 hasConcept C16005928 @default.
• W2007129218 hasConcept C163764329 @default.
• W2007129218 hasConcept C19218775 @default.
• W2007129218 hasConcept C203014093 @default.
• W2007129218 hasConcept C2776193487 @default.
• W2007129218 hasConcept C2776536667 @default.
• W2007129218 hasConcept C2777225697 @default.
• W2007129218 hasConcept C2777640609 @default.
• W2007129218 hasConcept C2778075117 @default.

• next