Matches in SemOpenAlex for { <https://semopenalex.org/work/W2008020599> ?p ?o ?g. }
Showing items 1 to 62 of
62
with 100 items per page.
- W2008020599 endingPage "S41" @default.
- W2008020599 startingPage "S35" @default.
- W2008020599 abstract "Hereditary angioedema (HAE), a rare but life-threatening condition, manifests as acute attacks of facial, laryngeal, genital, or peripheral swelling or abdominal pain secondary to intra-abdominal edema. Resulting from mutations affecting C1 esterase inhibitor (C1-INH), inhibitor of the first complement system component, attacks are not histamine-mediated and do not respond to antihistamines or corticosteroids. Low awareness and resemblance to other disorders often delay diagnosis; despite availability of C1-INH replacement in some countries, no approved, safe acute attack therapy exists in the United States. The biennial C1 Esterase Inhibitor Deficiency Workshops resulted from a European initiative for better knowledge and treatment of HAE and related diseases. This supplement contains work presented at the third workshop and expanded content toward a definitive picture of angioedema in the absence of allergy. Most notably, it includes cumulative genetic investigations; multinational laboratory diagnosis recommendations; current pathogenesis hypotheses; suggested prophylaxis and acute attack treatment, including home treatment; future treatment options; and analysis of patient subpopulations, including pediatric patients and patients whose angioedema worsened during pregnancy or hormone administration. Causes and management of acquired angioedema and a new type of angioedema with normal C1-INH are also discussed. Collaborative patient and physician efforts, crucial in rare diseases, are emphasized. This supplement seeks to raise awareness and aid diagnosis of HAE, optimize treatment for all patients, and provide a platform for further research in this rare, partially understood disorder." @default.
- W2008020599 created "2016-06-24" @default.
- W2008020599 creator A5004198892 @default.
- W2008020599 date "1990-01-01" @default.
- W2008020599 modified "2023-09-24" @default.
- W2008020599 title "Virus safe plasma proteins: Elimination of the viruses of risk by the manufacturing procedure" @default.
- W2008020599 cites W1966254060 @default.
- W2008020599 cites W1968873679 @default.
- W2008020599 cites W1976934646 @default.
- W2008020599 cites W1977282539 @default.
- W2008020599 cites W1991182388 @default.
- W2008020599 cites W2008791719 @default.
- W2008020599 cites W2043251422 @default.
- W2008020599 cites W2045677942 @default.
- W2008020599 cites W2053660971 @default.
- W2008020599 cites W2063446953 @default.
- W2008020599 cites W2100078961 @default.
- W2008020599 cites W2409242357 @default.
- W2008020599 cites W2411248931 @default.
- W2008020599 cites W2412982491 @default.
- W2008020599 cites W1991288670 @default.
- W2008020599 doi "https://doi.org/10.1016/0955-3886(90)90080-3" @default.
- W2008020599 hasPublicationYear "1990" @default.
- W2008020599 type Work @default.
- W2008020599 sameAs 2008020599 @default.
- W2008020599 citedByCount "0" @default.
- W2008020599 crossrefType "journal-article" @default.
- W2008020599 hasAuthorship W2008020599A5004198892 @default.
- W2008020599 hasConcept C16005928 @default.
- W2008020599 hasConcept C177713679 @default.
- W2008020599 hasConcept C203014093 @default.
- W2008020599 hasConcept C2777788586 @default.
- W2008020599 hasConcept C2777995640 @default.
- W2008020599 hasConcept C2779931649 @default.
- W2008020599 hasConcept C71924100 @default.
- W2008020599 hasConceptScore W2008020599C16005928 @default.
- W2008020599 hasConceptScore W2008020599C177713679 @default.
- W2008020599 hasConceptScore W2008020599C203014093 @default.
- W2008020599 hasConceptScore W2008020599C2777788586 @default.
- W2008020599 hasConceptScore W2008020599C2777995640 @default.
- W2008020599 hasConceptScore W2008020599C2779931649 @default.
- W2008020599 hasConceptScore W2008020599C71924100 @default.
- W2008020599 hasLocation W20080205991 @default.
- W2008020599 hasOpenAccess W2008020599 @default.
- W2008020599 hasPrimaryLocation W20080205991 @default.
- W2008020599 hasRelatedWork W2029716014 @default.
- W2008020599 hasRelatedWork W2071694201 @default.
- W2008020599 hasRelatedWork W2073647111 @default.
- W2008020599 hasRelatedWork W2089773927 @default.
- W2008020599 hasRelatedWork W2334745128 @default.
- W2008020599 hasRelatedWork W2594154015 @default.
- W2008020599 hasRelatedWork W2725954535 @default.
- W2008020599 hasRelatedWork W3118636652 @default.
- W2008020599 hasRelatedWork W4287218266 @default.
- W2008020599 hasRelatedWork W4367043352 @default.
- W2008020599 hasVolume "11" @default.
- W2008020599 isParatext "false" @default.
- W2008020599 isRetracted "false" @default.
- W2008020599 magId "2008020599" @default.
- W2008020599 workType "article" @default.