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- W2009063721 abstract "Les tests effectués dans le liquide céphalorachidien sont particulièrement utiles pour différencier les maladies à prions d’autres démences dégénératives ou d’autres encéphalopathies dont certaines potentiellement traitables. La recherche ou les dosages des protéines 14-3-3, tau ou S100b, utilisés, depuis plusieurs années, sont des marqueurs indirects qui ont une bonne sensibilité mais une spécificité qui est loin d’atteindre 100 %. La possibilité maintenant de mettre en évidence directement la protéine prion anormale au moyen d’une méthode d’amplification, la Real-Time Quaking-Induced Conversion (RT-QuIC), permet, surtout pour la forme sporadique de la maladie de Creutzfeldt–Jakob, une importante amélioration du diagnostic de probabilité. Même si ceci a conduit en 2017 à la modification des critères diagnostiques de surveillance, la RT-QuIC doit encore être considérée comme une technique de recherche.Tests performed in cerebrospinal fluid are particularly useful to differentiate prion diseases from other degenerative dementia or other encephalopathies eventually treatable. The detection or the assays of the 14-3-3, tau or S100b proteins, used for several years, remain indirect markers which have a good sensitivity but a specificity which is far from 100%. At present, the possibility to directly detect the abnormal prion protein using an amplification method, Real-Time Quaking-Induced Conversion (RT-QuIC), allows, especially for the sporadic form of Creutzfeldt–Jakob disease, a significant improvement for diagnosis probability. Although this led in 2017 to the modification of the diagnostic criteria for surveillance, RT-QuIC must still be considered as a research technique." @default.
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- W2009063721 date "2005-12-01" @default.
- W2009063721 modified "2023-10-16" @default.
- W2009063721 title "P1-7 Marqueurs biochimiques du liquide céphalo-rachidien et pathologies cognitives : l’expérience lilloise" @default.
- W2009063721 doi "https://doi.org/10.1016/s0035-3787(05)85323-8" @default.
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