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- W2010058090 abstract "Le protoxyde d’azote est largement utilisé en anesthésie. Il est réputé inoffensif mais peut avoir des effets indésirables lorsqu’il est utilisé au long cours ou de manière répétée. Nous rapportons ici une observation de sclérose combinée de la moelle iatrogène liée à une carence en vitamine B12.Un jeune homme drépanocytaire homozygote SS de 20 ans, régulièrement hospitalisé pour des crises vaso-occlusives sévères, présentait des signes déficitaires sensitivomoteurs ascendants, secondairement associés à des troubles sphinctériens. Il était initialement traité comme un syndrome de Guillain-Barré. Des symptômes neurologiques persistants permettaient de diagnostiquer une sclérose combinée de la moelle, secondaire à une carence en vitamine B12 induite par l’usage répété de protoxyde d’azote lors d’accès douloureux.L’utilisation large du protoxyde d’azote dans la prise en charge des crises vaso-occlusives drépanocytaires ne doit pas faire méconnaître ses risques potentiels notamment neurologiques.Nitrous oxide is widely used in anesthesia. It is usually safe but may be associated with severe side effects when it is used repeatedly or on a prolonged time. Here, we report a case of drug-induced subacute combined spinal cord degeneration related to cobalamin deficiency.A 20-year-old man with sickle-cell disease (SS) who was followed for severe recurrent vaso-occlusive crisis with repeated hospital admissions presented with ascending motor and sensitive neurological deficits that were later associated with bladder dysfunction. He was first considered to develop Guillain-Barre syndrome. However, persisting neurological signs despite adequate treatment lately led to diagnose subacute combined medullar degeneration due to abnormal cobalamin (vitamin B12) metabolism induced by repeated use of nitrous oxide during painful episodes of sickle-cell disease.Inhaled nitric oxide is widely used in the treatment of vaso-occlusive crisis. Clinicians should be aware of possible severe neurologic side effects." @default.
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- W2010058090 date "2014-04-01" @default.
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- W2010058090 title "Diagnostic de la carence en vitamine B12 en neurologie : à propos d’une série hospitalière" @default.
- W2010058090 doi "https://doi.org/10.1016/j.neurol.2014.01.115" @default.
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