Matches in SemOpenAlex for { <https://semopenalex.org/work/W2013200585> ?p ?o ?g. }
- W2013200585 endingPage "511" @default.
- W2013200585 startingPage "505" @default.
- W2013200585 abstract "Autosomal dominant polycystic kidney disease (ADPKD) is the most common genetic cause of end-stage renal disease, affecting approximately 1 in 1,000 people. The disease is characterized by the development of numerous large fluid-filled renal cysts over the course of decades. These cysts compress the surrounding renal parenchyma and impair its function. Mutations in two genes are responsible for ADPKD. The protein products of both of these genes, polycystin-1 and polycystin-2, localize to the primary cilium and participate in a wide variety of signaling pathways. Polycystin-1 undergoes several proteolytic cleavages that produce fragments which manifest biological activities. Recent results suggest that the production of polycystin-1 cleavage fragments is necessary and sufficient to account for at least some, although certainly not all, of the physiological functions of the parent protein." @default.
- W2013200585 created "2016-06-24" @default.
- W2013200585 creator A5004399124 @default.
- W2013200585 creator A5029633580 @default.
- W2013200585 creator A5037550900 @default.
- W2013200585 creator A5041557565 @default.
- W2013200585 creator A5049805706 @default.
- W2013200585 creator A5065846162 @default.
- W2013200585 date "2013-07-04" @default.
- W2013200585 modified "2023-09-23" @default.
- W2013200585 title "Polycystin-1 cleavage and the regulation of transcriptional pathways" @default.
- W2013200585 cites W1522763255 @default.
- W2013200585 cites W1965193260 @default.
- W2013200585 cites W1966685035 @default.
- W2013200585 cites W1967872597 @default.
- W2013200585 cites W1969887954 @default.
- W2013200585 cites W1970236704 @default.
- W2013200585 cites W1970264904 @default.
- W2013200585 cites W1975792086 @default.
- W2013200585 cites W1977332969 @default.
- W2013200585 cites W1979039650 @default.
- W2013200585 cites W1980851998 @default.
- W2013200585 cites W1981982858 @default.
- W2013200585 cites W1988146888 @default.
- W2013200585 cites W1992077718 @default.
- W2013200585 cites W1993017968 @default.
- W2013200585 cites W1995071144 @default.
- W2013200585 cites W1996655557 @default.
- W2013200585 cites W1998085149 @default.
- W2013200585 cites W1999818832 @default.
- W2013200585 cites W2000732162 @default.
- W2013200585 cites W2001536138 @default.
- W2013200585 cites W2005026678 @default.
- W2013200585 cites W2008647369 @default.
- W2013200585 cites W2010237592 @default.
- W2013200585 cites W2014264816 @default.
- W2013200585 cites W2014604277 @default.
- W2013200585 cites W2034042492 @default.
- W2013200585 cites W2034213169 @default.
- W2013200585 cites W2036588212 @default.
- W2013200585 cites W2037657846 @default.
- W2013200585 cites W2040190828 @default.
- W2013200585 cites W2047052174 @default.
- W2013200585 cites W2048209974 @default.
- W2013200585 cites W2053355175 @default.
- W2013200585 cites W2053632669 @default.
- W2013200585 cites W2058312756 @default.
- W2013200585 cites W2063191450 @default.
- W2013200585 cites W2068642486 @default.
- W2013200585 cites W2081437948 @default.
- W2013200585 cites W2081659168 @default.
- W2013200585 cites W2088811685 @default.
- W2013200585 cites W2093401766 @default.
- W2013200585 cites W2095869636 @default.
- W2013200585 cites W2096379342 @default.
- W2013200585 cites W2097214606 @default.
- W2013200585 cites W2097722745 @default.
- W2013200585 cites W2100704215 @default.
- W2013200585 cites W2103377139 @default.
- W2013200585 cites W2103483160 @default.
- W2013200585 cites W2105580120 @default.
- W2013200585 cites W2115926089 @default.
- W2013200585 cites W2117313136 @default.
- W2013200585 cites W2119367007 @default.
- W2013200585 cites W2133771702 @default.
- W2013200585 cites W2135100794 @default.
- W2013200585 cites W2135389531 @default.
- W2013200585 cites W2135979384 @default.
- W2013200585 cites W2136875701 @default.
- W2013200585 cites W2138009056 @default.
- W2013200585 cites W2138714101 @default.
- W2013200585 cites W2141452193 @default.
- W2013200585 cites W2142227033 @default.
- W2013200585 cites W2143261217 @default.
- W2013200585 cites W2144008673 @default.
- W2013200585 cites W2146671041 @default.
- W2013200585 cites W2148260879 @default.
- W2013200585 cites W2152299918 @default.
- W2013200585 cites W2153066126 @default.
- W2013200585 cites W2154435852 @default.
- W2013200585 cites W2154643490 @default.
- W2013200585 cites W2158079348 @default.
- W2013200585 cites W2161998042 @default.
- W2013200585 cites W2168415166 @default.
- W2013200585 cites W2169282327 @default.
- W2013200585 cites W3021964512 @default.
- W2013200585 cites W4256495376 @default.
- W2013200585 doi "https://doi.org/10.1007/s00467-013-2548-y" @default.
- W2013200585 hasPubMedCentralId "https://www.ncbi.nlm.nih.gov/pmc/articles/3844055" @default.
- W2013200585 hasPubMedId "https://pubmed.ncbi.nlm.nih.gov/23824180" @default.
- W2013200585 hasPublicationYear "2013" @default.
- W2013200585 type Work @default.
- W2013200585 sameAs 2013200585 @default.
- W2013200585 citedByCount "24" @default.
- W2013200585 countsByYear W20132005852014 @default.
- W2013200585 countsByYear W20132005852015 @default.
- W2013200585 countsByYear W20132005852016 @default.
- W2013200585 countsByYear W20132005852017 @default.