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- W2016070097 abstract "DEFINICION La atresia de vias biliares es una colangiopatia obstructiva neonatal, consecuencia de un proceso inflamatorio destructivo idiopatico que afecta a los conductos biliares intrahepaticos y extrahepaticos; esto conlleva a una fibrosis y obliteracion del tracto biliar con obstruccion del flujo y posterior desarrollo de una cirrosis biliar secundaria1-3. La atresia de vias biliares es una entidad poco frecuente, se estima que afecta a 1 de cada 12.000 nacidos vivos en el ambito mundial4. Sin embargo, es la causa mas frecuente de ictericia neonatal obstructiva extrahepatica y la causa mas frecuente de trasplante hepatico pediatrico de forma aislada2. Recientemente se han identificado dos fenotipos clinicos:" @default.
- W2016070097 created "2016-06-24" @default.
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- W2016070097 date "2003-01-01" @default.
- W2016070097 modified "2023-09-28" @default.
- W2016070097 title "Atresia de vías biliares" @default.
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- W2016070097 doi "https://doi.org/10.1016/s1695-4033(03)78021-7" @default.
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