Matches in SemOpenAlex for { <https://semopenalex.org/work/W2017996475> ?p ?o ?g. }
- W2017996475 abstract "Adrenocortical tumors (ACT) in children are very rare and are most frequently diagnosed in the context of the Li-Fraumeni syndrome, a multiple cancer syndrome linked to germline mutations of the tumor suppressor gene TP53 with loss of heterozygosity in the tumors. A peak of children ACT incidence is present in the states of southern Brazil, where they are linked to the high prevalence in the population of a specific TP53 mutation (R337H). Children ACT have specific features distinguishing them from adult tumors in their pathogenetic mechanisms, genomic profiles and prognosis. Epidemiological and molecular evidence suggests that in most cases they are derived from the fetal adrenal." @default.
- W2017996475 created "2016-06-24" @default.
- W2017996475 creator A5075849954 @default.
- W2017996475 creator A5084238877 @default.
- W2017996475 date "2015-02-18" @default.
- W2017996475 modified "2023-10-01" @default.
- W2017996475 title "Pediatric Adrenocortical Tumors: What They Can Tell Us on Adrenal Development and Comparison with Adult Adrenal Tumors" @default.
- W2017996475 cites W1251940471 @default.
- W2017996475 cites W1496877189 @default.
- W2017996475 cites W1592298195 @default.
- W2017996475 cites W1806278923 @default.
- W2017996475 cites W1926136904 @default.
- W2017996475 cites W1964350908 @default.
- W2017996475 cites W1964753012 @default.
- W2017996475 cites W1969330589 @default.
- W2017996475 cites W1969773394 @default.
- W2017996475 cites W1970399383 @default.
- W2017996475 cites W1971516997 @default.
- W2017996475 cites W1977936925 @default.
- W2017996475 cites W1979047631 @default.
- W2017996475 cites W1983254013 @default.
- W2017996475 cites W1983741506 @default.
- W2017996475 cites W1987416125 @default.
- W2017996475 cites W1988304079 @default.
- W2017996475 cites W1992384218 @default.
- W2017996475 cites W1993850600 @default.
- W2017996475 cites W1996133111 @default.
- W2017996475 cites W1997883660 @default.
- W2017996475 cites W1998702518 @default.
- W2017996475 cites W1999276992 @default.
- W2017996475 cites W2002793570 @default.
- W2017996475 cites W2002993576 @default.
- W2017996475 cites W2003721774 @default.
- W2017996475 cites W2004080531 @default.
- W2017996475 cites W2005542290 @default.
- W2017996475 cites W2006424575 @default.
- W2017996475 cites W2010743108 @default.
- W2017996475 cites W2012053348 @default.
- W2017996475 cites W2014424488 @default.
- W2017996475 cites W2015366457 @default.
- W2017996475 cites W2017530122 @default.
- W2017996475 cites W2017790495 @default.
- W2017996475 cites W2022560804 @default.
- W2017996475 cites W2025718398 @default.
- W2017996475 cites W2027355987 @default.
- W2017996475 cites W2029762798 @default.
- W2017996475 cites W2032999587 @default.
- W2017996475 cites W2035853338 @default.
- W2017996475 cites W2039590485 @default.
- W2017996475 cites W2039634774 @default.
- W2017996475 cites W2040263713 @default.
- W2017996475 cites W2040816499 @default.
- W2017996475 cites W2042271589 @default.
- W2017996475 cites W2044046815 @default.
- W2017996475 cites W2048028355 @default.
- W2017996475 cites W2049503985 @default.
- W2017996475 cites W2052196875 @default.
- W2017996475 cites W2057663570 @default.
- W2017996475 cites W2059880490 @default.
- W2017996475 cites W2063635264 @default.
- W2017996475 cites W2067098690 @default.
- W2017996475 cites W2068845486 @default.
- W2017996475 cites W2069472851 @default.
- W2017996475 cites W2071364196 @default.
- W2017996475 cites W2072268909 @default.
- W2017996475 cites W2077790055 @default.
- W2017996475 cites W2081672983 @default.
- W2017996475 cites W2085472231 @default.
- W2017996475 cites W2085761470 @default.
- W2017996475 cites W2088545698 @default.
- W2017996475 cites W2090940786 @default.
- W2017996475 cites W2090978506 @default.
- W2017996475 cites W2094943403 @default.
- W2017996475 cites W2095417135 @default.
- W2017996475 cites W2096758563 @default.
- W2017996475 cites W2098165008 @default.
- W2017996475 cites W2098622295 @default.
- W2017996475 cites W2100692201 @default.
- W2017996475 cites W2104542247 @default.
- W2017996475 cites W2106037975 @default.
- W2017996475 cites W2106919258 @default.
- W2017996475 cites W2107297624 @default.
- W2017996475 cites W2110985070 @default.
- W2017996475 cites W2114210346 @default.
- W2017996475 cites W2115615932 @default.
- W2017996475 cites W2116352768 @default.
- W2017996475 cites W2117116363 @default.
- W2017996475 cites W2120218419 @default.
- W2017996475 cites W2120961400 @default.
- W2017996475 cites W2123036315 @default.
- W2017996475 cites W2125417601 @default.
- W2017996475 cites W2127310589 @default.
- W2017996475 cites W2129110988 @default.
- W2017996475 cites W2130045814 @default.
- W2017996475 cites W2130311916 @default.
- W2017996475 cites W2135367483 @default.
- W2017996475 cites W2138551378 @default.
- W2017996475 cites W2139161464 @default.
- W2017996475 cites W2141197851 @default.
- W2017996475 cites W2144774255 @default.