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- W2019427404 startingPage "1483" @default.
- W2019427404 abstract "Box H/ACA ribonucleoproteins (RNPs), each consisting of one unique guide RNA and 4 common core proteins, constitute a family of complex enzymes that catalyze, in an RNA-guided manner, the isomerization of uridines to pseudouridines (Ψs) in RNAs, a reaction known as pseudouridylation. Over the years, box H/ACA RNPs have been extensively studied revealing many important aspects of these RNA modifying machines. In this review, we focus on the composition, structure, and biogenesis of H/ACA RNPs. We explain the mechanism of how this enzyme family recognizes and specifies its target uridine in a substrate RNA. We discuss the substrates of box H/ACA RNPs, focusing on rRNA (rRNA) and spliceosomal small nuclear RNA (snRNA). We describe the modification product Ψ and its contribution to RNA function. Finally, we consider possible mechanisms of the bone marrow failure syndrome dyskeratosis congenita and of prostate and other cancers linked to mutations in H/ACA RNPs." @default.
- W2019427404 created "2016-06-24" @default.
- W2019427404 creator A5004333869 @default.
- W2019427404 creator A5052224870 @default.
- W2019427404 date "2014-12-02" @default.
- W2019427404 modified "2023-10-13" @default.
- W2019427404 title "RNA-guided isomerization of uridine to pseudouridine—pseudouridylation" @default.
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