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- W2019946097 abstract "症例は78歳の女性である.MRIで両側前頭葉に白質病変をみとめ,認知機能障害,右片麻痺が進行し紹介入院となった.原因は特定されなかったがステロイドパルス療法にて病巣,症状ともに改善し退院した.3ヵ月後同症状が再燃,MRIで白質病巣が拡大し再入院となった.ステロイドパルス療法をおこなうも症状は進行した.MRI T2*画像と合わせ脳アミロイドアンギオパチー関連炎症(cerebral amyloid angiopathy related inflammation; CAA-I)と診断しシクロフォスファミド(CPA)パルス療法を2クール施行.白質病変とともに意識障害,片麻痺は改善し独歩にて退院した.わが国ではCAA-IへのCPA投与は報告がないが,ステロイド抵抗性のばあいは早期からもちいるべきものと思われる." @default.
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- W2019946097 date "2014-01-01" @default.
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- W2019946097 title "A case report of cerebral amyloid angiopathy-related inflammation treated with cyclophosphamide" @default.
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- W2019946097 doi "https://doi.org/10.5692/clinicalneurol.54.46" @default.
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