FRINK Linked Data Fragments server

Matches in SemOpenAlex for { <https://semopenalex.org/work/W2022882619> ?p ?o ?g. }

• W2022882619 endingPage "922" @default.
• W2022882619 startingPage "917" @default.
• W2022882619 abstract "X-linked adrenoleucodystrophy is a disorder occurring in different clinical forms, characterized by adrenal, gonadal and nervous system dysfunction. The basis of the illness is a derangement of the peroxisomal system necessary to oxidize very long-chain fatty acids that accumulate in various tissues. The diagnosis relies on clinical signs and symptoms and on biochemical findings. The six reported cases presented idiopathic adrenal insufficiency. We measured the lipid composition of red blood cell (RBC) ghosts of patients and control subjects. The distribution of phosphorus among phospholipid classes was unaffected; we could not demonstrate any differences between the fatty acid patterns of RBC membrane, either in total lipid extracts or in separated lipid classes. However, we found an increase in total lipid (both phospholipid and cholesterol), in membrane viscosity and in the Na+/K(+)-dependent ATPase. Therefore, we report four main findings on ghosts in adrenoleucodystrophy patients: (a) very long-chain fatty acids do not accumulate; (b) the lipid-protein ratio increases; (c) fluidity decreases; and (d) the activity of ATPase increases. The last finding is proposed as a possible biochemical marker of the illness. We conclude that adrenoleucodystrophy affects deeply RBC membranes." @default.
• W2022882619 created "2016-06-24" @default.
• W2022882619 creator A5009325923 @default.
• W2022882619 creator A5010251404 @default.
• W2022882619 creator A5049927005 @default.
• W2022882619 creator A5055286722 @default.
• W2022882619 creator A5090806401 @default.
• W2022882619 date "1996-10-01" @default.
• W2022882619 modified "2023-09-27" @default.
• W2022882619 title "Red blood cell ghosts are affected by adrenoleucodystrophy" @default.
• W2022882619 cites W1264549095 @default.
• W2022882619 cites W1513897103 @default.
• W2022882619 cites W1542881762 @default.
• W2022882619 cites W1900704054 @default.
• W2022882619 cites W1976030819 @default.
• W2022882619 cites W1991832287 @default.
• W2022882619 cites W1993086885 @default.
• W2022882619 cites W2004346519 @default.
• W2022882619 cites W2004567965 @default.
• W2022882619 cites W2012667579 @default.
• W2022882619 cites W2024526192 @default.
• W2022882619 cites W2033576172 @default.
• W2022882619 cites W2037167329 @default.
• W2022882619 cites W2037675553 @default.
• W2022882619 cites W2041698126 @default.
• W2022882619 cites W2042098378 @default.
• W2022882619 cites W2070783299 @default.
• W2022882619 cites W2086651117 @default.
• W2022882619 cites W2089183200 @default.
• W2022882619 cites W2104010651 @default.
• W2022882619 cites W2128635872 @default.
• W2022882619 cites W2135465528 @default.
• W2022882619 cites W2149371459 @default.
• W2022882619 cites W2166929619 @default.
• W2022882619 cites W2168526937 @default.
• W2022882619 cites W2221309829 @default.
• W2022882619 cites W4233938195 @default.
• W2022882619 cites W4243246213 @default.
• W2022882619 doi "https://doi.org/10.1111/j.1365-2362.1996.tb02138.x" @default.
• W2022882619 hasPubMedId "https://pubmed.ncbi.nlm.nih.gov/8911866" @default.
• W2022882619 hasPublicationYear "1996" @default.
• W2022882619 type Work @default.
• W2022882619 sameAs 2022882619 @default.
• W2022882619 citedByCount "4" @default.
• W2022882619 crossrefType "journal-article" @default.
• W2022882619 hasAuthorship W2022882619A5009325923 @default.
• W2022882619 hasAuthorship W2022882619A5010251404 @default.
• W2022882619 hasAuthorship W2022882619A5049927005 @default.
• W2022882619 hasAuthorship W2022882619A5055286722 @default.
• W2022882619 hasAuthorship W2022882619A5090806401 @default.
• W2022882619 hasConcept C104317684 @default.
• W2022882619 hasConcept C122398194 @default.
• W2022882619 hasConcept C126322002 @default.
• W2022882619 hasConcept C127078168 @default.
• W2022882619 hasConcept C134018914 @default.
• W2022882619 hasConcept C2776557347 @default.
• W2022882619 hasConcept C2777150068 @default.
• W2022882619 hasConcept C2778163477 @default.
• W2022882619 hasConcept C2778918659 @default.
• W2022882619 hasConcept C2779979121 @default.
• W2022882619 hasConcept C41625074 @default.
• W2022882619 hasConcept C543025807 @default.
• W2022882619 hasConcept C55493867 @default.
• W2022882619 hasConcept C71924100 @default.
• W2022882619 hasConcept C86803240 @default.
• W2022882619 hasConceptScore W2022882619C104317684 @default.
• W2022882619 hasConceptScore W2022882619C122398194 @default.
• W2022882619 hasConceptScore W2022882619C126322002 @default.
• W2022882619 hasConceptScore W2022882619C127078168 @default.
• W2022882619 hasConceptScore W2022882619C134018914 @default.
• W2022882619 hasConceptScore W2022882619C2776557347 @default.
• W2022882619 hasConceptScore W2022882619C2777150068 @default.
• W2022882619 hasConceptScore W2022882619C2778163477 @default.
• W2022882619 hasConceptScore W2022882619C2778918659 @default.
• W2022882619 hasConceptScore W2022882619C2779979121 @default.
• W2022882619 hasConceptScore W2022882619C41625074 @default.
• W2022882619 hasConceptScore W2022882619C543025807 @default.
• W2022882619 hasConceptScore W2022882619C55493867 @default.
• W2022882619 hasConceptScore W2022882619C71924100 @default.
• W2022882619 hasConceptScore W2022882619C86803240 @default.
• W2022882619 hasIssue "10" @default.
• W2022882619 hasLocation W20228826191 @default.
• W2022882619 hasLocation W20228826192 @default.
• W2022882619 hasOpenAccess W2022882619 @default.
• W2022882619 hasPrimaryLocation W20228826191 @default.
• W2022882619 hasRelatedWork W134354379 @default.
• W2022882619 hasRelatedWork W1980296475 @default.
• W2022882619 hasRelatedWork W1989598272 @default.
• W2022882619 hasRelatedWork W2009240753 @default.
• W2022882619 hasRelatedWork W2022882619 @default.
• W2022882619 hasRelatedWork W2047710690 @default.
• W2022882619 hasRelatedWork W2050472553 @default.
• W2022882619 hasRelatedWork W2057729851 @default.
• W2022882619 hasRelatedWork W2059387277 @default.
• W2022882619 hasRelatedWork W3021777942 @default.
• W2022882619 hasVolume "26" @default.
• W2022882619 isParatext "false" @default.
• W2022882619 isRetracted "false" @default.

• next