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- W2023178772 endingPage "927" @default.
- W2023178772 startingPage "911" @default.
- W2023178772 abstract "Since the original description of deficiency of the pulmonary surfactant in premature newborn infants by Avery and Mead in 1959, respiratory distress syndrome has most commonly been attributed to developmental immaturity of surfactant production. Studies of different ethnic groups, gender, targeted gene ablation in murine lineages, and recent clinical reports of monogenic causes of neonatal respiratory distress syndrome have demonstrated that genetic defects disrupt pulmonary surfactant metabolism and cause respiratory distress syndrome, especially in term or near-term infants and in older infants, children, and adults. In contrast to developmental causes of respiratory distress, which may improve as infants and children mature, genetic causes result in both acute and chronic (and potentially irreversible) respiratory failure." @default.
- W2023178772 created "2016-06-24" @default.
- W2023178772 creator A5008953665 @default.
- W2023178772 creator A5018295626 @default.
- W2023178772 creator A5036138403 @default.
- W2023178772 date "2006-10-01" @default.
- W2023178772 modified "2023-09-27" @default.
- W2023178772 title "Defects in Surfactant Synthesis: Clinical Implications" @default.
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