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- W2023195068 abstract "Microinjection of human liver mRNA from a patient homozygous for α1-antitrypsin deficiency (PiZZ) into Xenopus oocytes led to a 2–10-fold increase in lysosomal activity. Stimulation of lysosomal activity was not observed when mRNA from a normal human liver (α1-antitrypsin PiMM), or water was injected into the oocyte. This lysosomal activity was oocyte derived and was not due to translation products of the human liver mRNA. Thus a protein that accumulates intracellularly in the secretory pathway is capable of stimulating lysosomal activity." @default.
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- W2023195068 date "1985-04-22" @default.
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- W2023195068 title "Human Z α<sub>1</sub> -antitrypsin accumulates intracellularly and stimulates lysosomal activity when synthesised in the <i>Xenopus</i> oocyte" @default.
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- W2023195068 doi "https://doi.org/10.1016/0014-5793(85)80798-5" @default.
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