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- W2023773575 startingPage "1571" @default.
- W2023773575 abstract "CREUTZFELDT–JAKOB disease (CJD), kuru, and the Gerstmann–Sträussler syndrome are human neurodegenerative diseases that can be transmitted experimentally to animals. In 1920, Creutzfeldt described a progressive dementing illness in a 22-year-old woman. The following year, Jakob described four older patients with a clinically similar presentation and course.1 During the ensuing four decades, numerous cases of CJD were described clinically and pathologically. Although most cases of CJD present with a progressive dementia characterized initially by loss of memory, diminished intellect, and poor judgment, a few cases present as progressive cerebellar syndromes, with diminished coordination, tremor, and ataxia. Patients with the ataxic form . . ." @default.
- W2023773575 created "2016-06-24" @default.
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- W2023773575 creator A5066991343 @default.
- W2023773575 date "1987-12-17" @default.
- W2023773575 modified "2023-10-03" @default.
- W2023773575 title "Prions and Neurodegenerative Diseases" @default.
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- W2023773575 doi "https://doi.org/10.1056/nejm198712173172505" @default.
- W2023773575 hasPubMedId "https://pubmed.ncbi.nlm.nih.gov/3317055" @default.
- W2023773575 hasPublicationYear "1987" @default.
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