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- W2025172111 abstract "La maladie de Paget vulvaire est divisée en trois types selon son origine. Elle peut être vulvaire primitive (type 1), liée à un adénocarcinome non cutané, colorectal ou cervical (type 2) ou à un carcinome urothélial (type 3). Les lésions in situ de type 1 doivent être considérées comme potentiellement infiltrantes. Leur immunophénotype est CK7+ / CK20–. Classiquement, en cas d’invasion d’épaisseur inférieure à 1 mm, les métastases ganglionnaires sont exceptionnelles. Nous rapportons l’observation d’une femme, ménopausée, souffrant d’une maladie de Paget de type 1 avec invasion superficielle et métastases ganglionnaires inguinales multiples. Vulvar Paget's disease is sub-classified into three types based upon its origin. It might be a primary vulvar disease (type 1) or associated with a non-cutaneous adenocarcinoma–rectal, colonic, cervical (type 2) or linked with an urothelial neoplasia (type 3). Type 1 lesions must be considered as potentially invasive. Their immunophenotype is CK7+ / CK20–. Classically, in case of depth of invasion below 1 mm, nodal metastases are exceptional. We report a case of type 1 Paget's disease in a postmenopausal woman with superficial invasion and multiple inguinal nodal metastases." @default.
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- W2025172111 date "2011-10-01" @default.
- W2025172111 modified "2023-10-16" @default.
- W2025172111 title "Maladie de Paget vulvaire micro-invasive et métastase ganglionnaire : une même maladie ?" @default.
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- W2025172111 doi "https://doi.org/10.1016/j.annpat.2011.06.003" @default.
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