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- W2028918872 abstract "It has been shown recently that Kasabach-Merritt phenomenon, the association of a vascular tumour and consumption coagulopathy, does not--as previously thought--complicate classical infantile hemangiomas but distinctive entities called kaposiform hemangioendothelioma (KHE) and tufted angioma (TA), both tumours on the same neoplastic spectrum. These tumours have been found in the neck, face, thorax, abdomen, retroperitoneum and limbs and are associated with a mortality rate of as high as 30 %. Several therapeutic modalities, including alpha-interferon, vincristine, radiotherapy and surgery have been reported in the literature. We report a case of retroperitoneal kaposiform hemangioendothelioma regression using alpha-interferon and discuss the current knowledge of this entity and its treatment." @default.
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- W2028918872 date "2006-10-01" @default.
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- W2028918872 title "Successful Management of a Retroperitoneal Kaposiform Hemangioendothelioma with Kasabach-Merritt Phenomenon Using α-Interferon" @default.
- W2028918872 doi "https://doi.org/10.1055/s-2006-924615" @default.
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