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- W2031500733 abstract "Abstract Cultured skin fibroblasts from 6 patients with Niemann-Pick disease type A were investigated for cholesterol metabolism. An increase in cholesterol synthesis from 14C-sodium acetate was observed in all cases. A decrease in 14C-oleic acid incorporation into cholesteryl esters was found in 5 of 6 cases. 125I-low density lipoprotein binding was significantly reduced in 3 of 4 investigated cases." @default.
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- W2031500733 date "1981-09-01" @default.
- W2031500733 modified "2023-09-26" @default.
- W2031500733 title "Changes in cholesterol metabolism in cultured fibroblasts from patients with Niemann-Pick disease" @default.
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- W2031500733 doi "https://doi.org/10.1016/0006-291x(81)91496-0" @default.
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