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- W2035745908 abstract "結節性多発性動脈炎(PN)に血栓性血小板減少性紫斑病(TTP)を合併した本邦第1例目を報告する.症例は70才の女性.再発性多発性脳神経炎(左第II・V,右第VIII・IX・X脳神経障害)で発病し,経過中にTTPを合併して出血傾向が出現し,全経過約11カ月で死亡した.主要病理学的所見は結節形成を伴う壊死性動脈炎と諸臓器における出血および微小血栓であり, PNにTTPを合併したことが死因と考えられた. PNの診断においてTTPは必須の除外疾患であるが,本症例は両者の合併が起こりえることを示した.さらに,本症例では脳神経の神経上膜から神経束への炎症細胞浸潤を認め,この所見はPNにおける末梢神経障害機序として血管炎とともに重視すべき所見と思われた." @default.
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- W2035745908 date "1986-01-01" @default.
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- W2035745908 title "An autopsy case of polyarteritis nodosa associated with multiple cranial neuritis and thrombotic thrombocytopenic purpura." @default.
- W2035745908 doi "https://doi.org/10.2169/naika.75.1291" @default.
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