Matches in SemOpenAlex for { <https://semopenalex.org/work/W2039457265> ?p ?o ?g. }
- W2039457265 abstract "Liver transplantation provides an effective means for replacing a failing liver, in addition to correcting the underlying abnormality in many metabolic disorders. Results of liver transplantation for metabolic diseases have been generally encouraging, with the exception of hereditary hemochromatosis, in which infectious and cardiac complications appear to increase post-transplant mortality. Better pretransplant diagnosis of hemochromatosis, utilizing the recently identified putative gene, may help reduce post-transplant complications. In metabolic diseases, improved understanding of the underlying genetic and molecular defects will lead to advances in medical therapy and perhaps a decreased need for liver transplantation. NTBC therapy for hereditary tyrosinemia and purified glucocerebroside therapy for Gaucher disease are two such examples. The prospects of gene therapy are being actively pursued for many metabolic diseases, such as CF, hemophilia, and familial hypercholesterolemia. Until such investigation leads directly to clinical practice, however, liver transplantation remains an effective option for therapy for a wide range of metabolic diseases." @default.
- W2039457265 created "2016-06-24" @default.
- W2039457265 creator A5019804029 @default.
- W2039457265 creator A5091028785 @default.
- W2039457265 date "1997-08-01" @default.
- W2039457265 modified "2023-09-27" @default.
- W2039457265 title "LIVER TRANSPLANTATION FOR HEMOCHROMATOSIS, WILSON'S DISEASE, AND OTHER METABOLIC DISORDERS" @default.
- W2039457265 cites W134514304 @default.
- W2039457265 cites W1508187979 @default.
- W2039457265 cites W1508281538 @default.
- W2039457265 cites W1552944085 @default.
- W2039457265 cites W158502641 @default.
- W2039457265 cites W1594724806 @default.
- W2039457265 cites W1612407641 @default.
- W2039457265 cites W1630615775 @default.
- W2039457265 cites W1695754907 @default.
- W2039457265 cites W1825881666 @default.
- W2039457265 cites W1890293889 @default.
- W2039457265 cites W1911278408 @default.
- W2039457265 cites W1971965818 @default.
- W2039457265 cites W1974134468 @default.
- W2039457265 cites W1978558019 @default.
- W2039457265 cites W1979097055 @default.
- W2039457265 cites W1979887660 @default.
- W2039457265 cites W1983678584 @default.
- W2039457265 cites W1985187522 @default.
- W2039457265 cites W1985864332 @default.
- W2039457265 cites W1986448490 @default.
- W2039457265 cites W1986563833 @default.
- W2039457265 cites W1987218750 @default.
- W2039457265 cites W1987447922 @default.
- W2039457265 cites W1988042250 @default.
- W2039457265 cites W1988192574 @default.
- W2039457265 cites W1988934234 @default.
- W2039457265 cites W1989120847 @default.
- W2039457265 cites W1991539040 @default.
- W2039457265 cites W1991572447 @default.
- W2039457265 cites W1992611128 @default.
- W2039457265 cites W2000460828 @default.
- W2039457265 cites W2002023508 @default.
- W2039457265 cites W2002605005 @default.
- W2039457265 cites W2002928840 @default.
- W2039457265 cites W2004673922 @default.
- W2039457265 cites W2005642726 @default.
- W2039457265 cites W2007315507 @default.
- W2039457265 cites W2009961383 @default.
- W2039457265 cites W2012772935 @default.
- W2039457265 cites W2014031811 @default.
- W2039457265 cites W2015206296 @default.
- W2039457265 cites W2015449233 @default.
- W2039457265 cites W2016691772 @default.
- W2039457265 cites W2024544489 @default.
- W2039457265 cites W2024950199 @default.
- W2039457265 cites W2025743343 @default.
- W2039457265 cites W2026599665 @default.
- W2039457265 cites W2027151038 @default.
- W2039457265 cites W2028250846 @default.
- W2039457265 cites W2035763999 @default.
- W2039457265 cites W2036204884 @default.
- W2039457265 cites W2036760330 @default.
- W2039457265 cites W2038528361 @default.
- W2039457265 cites W2038800862 @default.
- W2039457265 cites W2040947899 @default.
- W2039457265 cites W2042308806 @default.
- W2039457265 cites W2043403105 @default.
- W2039457265 cites W2045299448 @default.
- W2039457265 cites W2045690727 @default.
- W2039457265 cites W2049004325 @default.
- W2039457265 cites W2050212047 @default.
- W2039457265 cites W2052779919 @default.
- W2039457265 cites W2061582847 @default.
- W2039457265 cites W2061900539 @default.
- W2039457265 cites W2061909665 @default.
- W2039457265 cites W2062580179 @default.
- W2039457265 cites W2067356518 @default.
- W2039457265 cites W2070895182 @default.
- W2039457265 cites W2073378867 @default.
- W2039457265 cites W2074092452 @default.
- W2039457265 cites W2077420903 @default.
- W2039457265 cites W2079947477 @default.
- W2039457265 cites W2081633304 @default.
- W2039457265 cites W2086029751 @default.
- W2039457265 cites W2086110416 @default.
- W2039457265 cites W2090596092 @default.
- W2039457265 cites W2092246531 @default.
- W2039457265 cites W2109138583 @default.
- W2039457265 cites W2109425311 @default.
- W2039457265 cites W2113041802 @default.
- W2039457265 cites W2115598881 @default.
- W2039457265 cites W2133286465 @default.
- W2039457265 cites W2137766764 @default.
- W2039457265 cites W2141835142 @default.
- W2039457265 cites W2146216642 @default.
- W2039457265 cites W2152762927 @default.
- W2039457265 cites W2153880803 @default.
- W2039457265 cites W2170935875 @default.
- W2039457265 cites W2274433621 @default.
- W2039457265 cites W2285401534 @default.
- W2039457265 cites W2314218964 @default.
- W2039457265 cites W2325223078 @default.