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- W2041025400 abstract "Les encéphalopathies subaiguës spongiformes transmissibles sont des maladies neurodégénératives dont les agents étiologiques, les ATNC, sont encore inconnus. La théorie du prion postule que ces agents seraient composés exclusivement d'une protéine de l'hôte, la PrP, sous une conformation pathologique sans modification de la séquence primaire en acides aminés. Les ATNC sont particulièrement résistants aux procédés d'inactivation chimiques et physiques, et peuvent persister dans l'environnement pendant plusieurs années. Par ailleurs, ces agents sont capables de franchir les barrières d'espèce, comme le montre l'émergence de la nouvelle variante de la maladie de Creutzfeldt-Jakob induite par l'exposition de la population humaine à l'agent de l'encéphalopathie spongiforme bovine. Transmissible spongiform encephalopathies are neurodegenerative diseases caused by unknown transmissible agents (TSE agents), also called prions. Prion theory postulates that TSE agents are composed of a single host-encoded protein (PrP) under an abnormal tridimensional structure, without any modification of the primary sequence. TSE agents are resistant to all procedures that usually inactivate microorganisms and can persist years in the environment. Moreover, these agents can cross species barriers, as demonstrated by the occurrence of the new variant Creutzfeldt-Jakob disease in the United Kingdom, which is now recognised to be induced by the BSE agent." @default.
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- W2041025400 date "2001-03-01" @default.
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- W2041025400 title "Les encéphalopathies subaiguës spongiformes transmissibles ou maladies à prions" @default.
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- W2041025400 doi "https://doi.org/10.1016/s0399-077x(01)80069-x" @default.
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