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- W2041648936 abstract "La granulomatose septique chronique (GSC) est un déficit immunitaire primitif d’origine génétique, consécutif à un défaut du métabolisme oxydatif des phagocytes. Elle se caractérise par des infections bactériennes et fongiques répétées. Nous rapportons le cas d’un nourrisson de deux mois hospitalisé pour une ostéomyélite à Serratia marcescens d’un métacarpien ayant révélé une GSC. Bien que rare, la GSC doit être évoquée en cas d’infection inhabituelle ou atypique. Chronic granulomatous disease is a rare, primary immunodeficiency disorder characterized by a defect in oxidative metabolism in phagocytes and recurrent bacterial and fungal infections. We report a case in a 2-month-old infant admitted with metacarpic osteomyelitis due to Serratia marcescens. Chronic granulomatous disease is rare but must be considered in cases of uncommon or atypical infection." @default.
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- W2041648936 date "2014-07-01" @default.
- W2041648936 modified "2023-09-27" @default.
- W2041648936 title "Granulomatose septique chronique révélée par une ostéomyélite à Serratia marcescens" @default.
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- W2041648936 doi "https://doi.org/10.1016/j.arcped.2014.04.023" @default.
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