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- W2041938961 abstract "Aortic aneurysm is common, accounting for 1-2% of all deaths in industrialized countries. Early theories of the causes of human aneurysm mostly focused on inherited or acquired defects in components of the extracellular matrix in the aorta. Although several mutations in the genes encoding extracellular matrix proteins have been recognized, more recent discoveries have shown important perturbations in cytokine signalling cascades and intracellular components of the smooth muscle contractile apparatus. The modelling of single-gene heritable aneurysm disorders in mice has shown unexpected involvement of the transforming growth factor-β cytokine pathway in aortic aneurysm, highlighting the potential for new therapeutic strategies." @default.
- W2041938961 created "2016-06-24" @default.
- W2041938961 creator A5038027788 @default.
- W2041938961 creator A5048066616 @default.
- W2041938961 date "2011-05-01" @default.
- W2041938961 modified "2023-10-10" @default.
- W2041938961 title "Lessons on the pathogenesis of aneurysm from heritable conditions" @default.
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