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- W2049649845 abstract "Os autores relatam dois casos de amiotrofia espinal infantil, confirmados por exame eletroneuromiográfico, que evoluiram de forma atípica. No primeiro, criança do sexo feminino de 10 anos de idade, a sintomatologia motora foi de predomínio distal. No outro, paciente do sexo feminino de 7 anos de idade, o quadro foi rapidamente progressivo em 4 meses, ocorrendo óbito após 10 meses. São apresentadas as classificações mais aceitas da doença, discutindo-se a caracterização da forma clínica apresentada por nossos pacientes." @default.
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- W2049649845 date "1993-09-01" @default.
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- W2049649845 title "Amiotrofia espinal infantil com evolução atípica relato de dois casos: report of two cases" @default.
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- W2049649845 doi "https://doi.org/10.1590/s0004-282x1993000300020" @default.
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