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- W2051204391 endingPage "180" @default.
- W2051204391 startingPage "163" @default.
- W2051204391 abstract "Duchenne's progressive muscular dystrophy (DMD) is a genetic muscle disorder that causes degeneration and atrophy of the systemic and cardiac muscle. The disease is manifested early in childhood, and most of patients die by age 20 years of respiratory failure or heart failure. The cardiac involvement in DMD is characterized pathologically by degeneration and fibrosis of the myocardium, centering around the posterolateral wall of the left ventricle. Functionally, an abnormal electrocardiogram, valve motion, wall thickness, and wall motion are observed. Furthermore, abnormalities in plasma levels of atrial natriuretic peptide and autonomic function are also demonstrated. In this review, the cardiac involvements in DMD in the following aspects are described: 1) Electrocardiogram; a) high-frequency notches on the QRS complexes, b) amplitude of QRS complexes, c) late potential, d) arrhythmias, e) heart rate variability, f) a 10-year follow-up study, 2) Echocardiographic findings, 3) Hemodynamic findings, 4) Atrial natriuretic peptide." @default.
- W2051204391 created "2016-06-24" @default.
- W2051204391 creator A5063239378 @default.
- W2051204391 date "1997-01-01" @default.
- W2051204391 modified "2023-10-14" @default.
- W2051204391 title "Cardiac Involvement in Progressive Muscular Dystrophy of the Duchenne Type." @default.
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- W2051204391 doi "https://doi.org/10.1536/ihj.38.163" @default.
- W2051204391 hasPubMedId "https://pubmed.ncbi.nlm.nih.gov/9201104" @default.
- W2051204391 hasPublicationYear "1997" @default.