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- W2051205604 abstract "Revisar los hallazgos radiológicos del carcinoma adenoide quístico (CAQ), así como su presentación clínica. Realizamos un estudio retrospectivo desde enero de 1990 hasta julio de 2004, en el que se encontraron 5 casos de CAQ de mama, todos ellos en mujeres, entre 4.036 lesiones malignas diagnosticadas (0,12%). Se revisaron los estudios mamográficos disponibles (5 casos), ecográficos (4 casos) y de resonancia magnética (un caso). Asimismo se revisó la presentación clínica de los casos y la evolución de las pacientes. Tres casos fueron palpables. Los hallazgos mamográficos consistieron en tres nódulos irregulares y mal delimitados, un nódulo redondeado bien delimitado y una densidad asimétrica. En ningún caso se apreciaron microcalcificaciones. En tres casos la ecografía mostró la presencia de nódulos polilobulados y mal delimitados, mientras que otra de las lesiones apareció como un nódulo redondeado y bien delimitado con pequeños quistes en su interior. Esta lesión presentó una intensa vascularización en el estudio doppler. El único caso en que se realizó resonancia magnética mostró un nódulo redondeado con captación heterogénea de contraste, márgenes bien definidos y curva de captación altamente sospechosa de malignidad. El tratamiento aplicado en todos los casos fue la tumorectomía asociada a radioterapia. Cuatro de las pacientes se encuentran asintomáticas hasta el momento (seguimiento medio de 64 meses) y una de ellas presentó metastasis pulmonares y hepáticas 12 años después del diagnóstico de CAQ. El CAQ es una tumoración infrecuente de mama cuya apariencia radiológica es variada, aunque predominan lesiones de moderada o alta sospecha. Destacamos la ausencia de microcalcificaciones en estos tumores. Generalmente su pronóstico es bueno, aunque existe la posibilidad de desarrollar metástasis a distancia. To review the clinical presentation and imaging findings of adenoid cystic carcinoma (ACC). We performed a retrospective study of the period between January 1990 and July 2004, comprising five cases of ACC of the breast, all in women, among 4,036 malignant lesions diagnosed (0.12%). We reviewed the available imaging studies (mammography in all five cases, ultrasound in four, and magnetic resonance in one). We also reviewed the clinical presentation and evolution in all patients. Three patients presented with palpable lesions. Mammographic findings consisted of irregular, ill-defined nodules in three cases, a well-defined rounded nodule in one, and an asymmetrical density in the other. No microcalcifications were observed in any case. Ultrasound examination showed ill-defined polylobulated nodules in three cases and a well-defined, rounded nodule with small cysts inside in the remaining case that showed intense vascularization in the Doppler study. The only case studied by magnetic resonance was seen as a rounded nodule that showed heterogeneous contrast uptake, well-defined margins, and an enhancement curve considered highly suspicious for malignancy. Treatment was tumorectomy together with radiotherapy in all cases. Four patients remain asymptomatic at present (mean follow-up = 64 months) and one presented lung and liver metastes twelve years after the diagnosis of ACC. ACC is an uncommon breast tumor with varied radiologic appearance, although moderately or highly suspicious lesions predominate. We consider the absence of microcalcifications in these tumors to be noteworthy. The prognosis is generally good, although the possibility of remote metastasis exists." @default.
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- W2051205604 date "2006-07-01" @default.
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- W2051205604 title "Carcinoma adenoide quístico de mama" @default.
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- W2051205604 doi "https://doi.org/10.1016/s0033-8338(06)73160-5" @default.
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