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- W2055673485 abstract "Most coagulation abnormalities found in individuals with systemic lupus erythematosus (SLE) are related to the production of anti-phospholipid antibody, which causes thrombotic or thromboembolic events. On the other hand, thrombotic thrombocytopenic purpura (TTP), characterized by microangiopathic hemolytic anemia, thrombocytopenia, renal dysfunction, fever, and neurologic symptoms, is an extremely rare event during the clinical course of SLE. Only four cases of clinical and histopathological TTP were identified among the 257 patients with SLE who underwent renal biopsy [ [1] Manadan A.M. Harris C. Schwartz M.M. Block J.A. The frequency of thrombotic thrombocytopenic purpura in patients with systemic lupus erythematosus undergoing kidney biopsy. J Rheumatol. 2003; 30: 1227-1230 PubMed Google Scholar ]. Early recognition and treatment interventions such as plasma exchange are required for this life-threatening disease." @default.
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- W2055673485 date "2010-11-01" @default.
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- W2055673485 title "Successful treatment of thrombotic thrombocytopenic purpura associated with systemic lupus erythematosus with recombinant human soluble thrombomodulin" @default.
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- W2055673485 doi "https://doi.org/10.1016/j.thromres.2010.06.024" @default.
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