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- W2055861064 abstract "El neurólogo debe anticipar y reconocer el inicio de la insuficiencia respiratoria en los pacientes neuromusculares. La sintomatología varía en función de la velocidad de instauración de la debilidad de la musculatura respiratoria. Las situaciones de catástrofe suelen acontecer en 3 supuestos clínicos: 1) manejo incorrecto de una insuficiencia respiratoria aguda de origen neuromuscular, disautonomía o durante una anestesia general a pacientes neuromusculares; 2) pronóstico y tratamiento erróneos por falta de un diagnóstico acertado; esta situación es más frecuente en pacientes críticos dependientes de un ventilador con debilidad muscular asociada, en el diferencial de neuropatías agudas o enfermedad de la neurona motora, y 3) inadecuada actuación médica en el paciente neuromuscular con diagnóstico definido, pero con larga evolución (esclerosis lateral amiotrófica, atrofia muscular espinal, distrofia miotónica y otras distrofias musculares). Neurologists should anticipate and recognize the onset of respiratory failure in patients with neuromuscular diseases. Symptoms vary according to the speed of onset of respiratory muscle weakness. Catastrophic situations usually occur in three clinical scenarios: 1) incorrect management of acute respiratory failure of neuromuscular origin, autonomic dysfunction or during general anaesthesia of patients with neuromuscular diseases ; 2) incorrect prognosis and treatment due to the lack of a correct diagnosis. This situation is more common in ventilated patients with associated muscular weakness, acute neuropathies or motor neuron disease, and 3) inappropriate medical intervention in patients with neuromuscular disease with a definitive diagnosis but longstanding disease (amyotrophic lateral sclerosis, spinal muscular atrophy, myotonic dystrophy and other muscular dystrophies)." @default.
- W2055861064 created "2016-06-24" @default.
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- W2055861064 date "2010-10-01" @default.
- W2055861064 modified "2023-09-29" @default.
- W2055861064 title "Enfermedades neuromusculares catastrófi cas" @default.
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- W2055861064 doi "https://doi.org/10.1016/s0213-4853(10)70049-9" @default.
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