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- W2056229704 abstract "Familial renal cancer (FRC) is a heterogeneous disorder comprised of a variety of subtypes. Each subtype is known to have unique histologic features, genetic alterations, and response to therapy. Through the study of families affected by hereditary forms of kidney cancer, insights into the genetic basis of this disease have been identified. This has resulted in the elucidation of a number of kidney cancer gene pathways. Study of these pathways has led to the development of novel targeted molecular treatments for patients affected by systemic disease. As a result, the treatments for families affected by von Hippel-Lindau (VHL), hereditary papillary renal carcinoma (HPRC), hereditary leiomyomatosis renal cell carcinoma (HLRCC), and Birt-Hogg-Dubé (BHD) are rapidly changing. We review the genetics and contemporary surgical management of familial forms of kidney cancer." @default.
- W2056229704 created "2016-06-24" @default.
- W2056229704 creator A5004211801 @default.
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- W2056229704 creator A5009060794 @default.
- W2056229704 creator A5062324742 @default.
- W2056229704 creator A5077264017 @default.
- W2056229704 date "2011-01-01" @default.
- W2056229704 modified "2023-10-13" @default.
- W2056229704 title "Familial Renal Cancer: Molecular Genetics and Surgical Management" @default.
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- W2056229704 doi "https://doi.org/10.1155/2011/658767" @default.