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- W2056595486 endingPage "429" @default.
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- W2056595486 abstract "Organic acid analysis is a powerful technique in the diagnosis of inborn errors of metabolism. Since the development of the technique over twenty-five years ago, it has evolved into a sophisticated and powerful method and is an essential tool in the diagnosis of the organic acidurias. The chemistry and biochemistry of organic acids, as well as sample preparation, instrumentation, and many aspects of the more commonly used methods for the analysis of these compounds, are reviewed. The biochemical and clinical characteristics of each of the primary organic acidurias are described. In addition, the various noninherited causes of secondary organic acidurias that lead to the excretion of abnormal organic acids are also described, and ways of differentiating primary from secondary causes are discussed." @default.
- W2056595486 created "2016-06-24" @default.
- W2056595486 creator A5049280234 @default.
- W2056595486 creator A5076507842 @default.
- W2056595486 date "1995-01-01" @default.
- W2056595486 modified "2023-09-23" @default.
- W2056595486 title "Organic Acidurias and Related Abnormalities" @default.
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